{"id":2010,"date":"2025-12-11T15:05:48","date_gmt":"2025-12-11T12:05:48","guid":{"rendered":"https:\/\/wiki.dev.voka.io\/diseases\/uncategorized\/tumores-do-plexo-coroide\/"},"modified":"2025-12-11T15:05:55","modified_gmt":"2025-12-11T12:05:55","slug":"tumores-do-plexo-coroide","status":"publish","type":"diseases_post","link":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/","title":{"rendered":"Tumores do plexo coroide: papiloma e carcinoma \u2013 etiologia, classifica\u00e7\u00e3o e tratamento"},"content":{"rendered":"<p><?xml encoding=\"UTF-8\" ?><\/p>\n<p>O plexo coroide produz o l\u00edquor (l\u00edquido cefalorraquidiano) e est\u00e1 localizado nos ventr\u00edculos cerebrais. A localiza\u00e7\u00e3o do tumor depende da idade: em crian\u00e7as, os ventr\u00edculos laterais s\u00e3o afetados com mais frequ\u00eancia, enquanto em adultos, o \u00f3rg\u00e3o mais afetado \u00e9 o quarto ventr\u00edculo. <\/p>\n<p><strong>O papiloma do plexo coroide<\/strong> (PPC) \u00e9 um tumor benigno do epit\u00e9lio do plexo coroide do c\u00e9rebro: \u00e9 classificado como grau I, de acordo com a classifica\u00e7\u00e3o da OMS (WHO Grade 1). Este \u00e9 o tumor mais comum do plexo coroide.<\/p>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp\" alt=\"Papiloma do plexo coroide no quarto ventr\u00edculo.\"><figcaption class=\"wp-element-caption\">Papiloma do plexo coroide no quarto ventr\u00edculo \u2013 <a href=\"https:\/\/catalog.voka.io\/en\/models\/cec5f80b-babf-4f02-ab97-355cf37c21ad\/95bcd6fa-2d66-476f-88bf-66e25519f4c9\/1b81e9e6-db72-4320-ace3-54319fac1292\/b3439e1b-466c-4922-9611-e6f42ca05078\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">Modelo 3D<\/a><\/figcaption><\/figure>\n<p><strong>Carcinoma do plexo coroide (CPC)<\/strong> \u00e9 um tumor raro e altamente maligno (WHO Grade 3) que se origina no epit\u00e9lio do plexo coroide dos ventr\u00edculos cerebrais. \u00c9 diagnosticado predominantemente em crian\u00e7as menores de 5 anos de idade , sendo caracterizado por curso agressivo, pela tend\u00eancia \u00e0 invas\u00e3o, pela met\u00e1stase no sistema nervoso central e pelo progn\u00f3stico extremamente desfavor\u00e1vel.<\/p>\n<h2 class=\"wp-block-heading\" id=\"etiologia-e-epidemiologia-do-tumor\"><strong>Etiologia e epidemiologia do tumor <\/strong><strong><\/strong><\/h2>\n<h3 class=\"wp-block-heading\" id=\"etiologia-e-fatores-geneticos\"><strong>Etiologia e fatores gen\u00e9ticos<\/strong><\/h3>\n<p>As causas exatas do PPC s\u00e3o desconhecidas. O PPC n\u00e3o \u00e9 caracterizado por muta\u00e7\u00f5es drivers, mas alguns casos est\u00e3o associados a s\u00edndromes gen\u00e9ticas raras, como a s\u00edndrome de Aicardi.<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Formas at\u00edpicas (aPPC) e malignas (CPC):<\/strong> podem ocorrer devido a muta\u00e7\u00f5es do TP53, especialmente em crian\u00e7as com a s\u00edndrome de Li-Fraumeni.<\/li>\n<li>A maioria (at\u00e9 60%) dos pacientes com o CPC apresenta uma muta\u00e7\u00e3o som\u00e1tica do TP53 e, em 40% dos casos, o tumor est\u00e1 associado \u00e0 s\u00edndrome de Li-Fraumeni (LFS), causada por uma muta\u00e7\u00e3o germinativa do <em>TP53<\/em>.<\/li>\n<li>Em alguns casos, s\u00e3o detectadas outras anormalidades em genes que controlam o ciclo celular (por exemplo, <em>PTEN, CDKN2A<\/em>).<\/li>\n<\/ul>\n<h3 class=\"wp-block-heading\" id=\"epidemiologia\"><strong>Epidemiologia<\/strong><\/h3>\n<p>As caracter\u00edsticas epidemiol\u00f3gicas dos tumores do plexo coroide devem-se \u00e0 sua baixa incid\u00eancia e \u00e0 forte depend\u00eancia da idade do paciente.<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Incid\u00eancia:<\/strong> Os tumores do plexo coroide s\u00e3o tumores raros (menos de 1% de todos os tumores intracranianos). Em crian\u00e7as menores de 1 ano de idade, esses tumores representam at\u00e9 10-15% de todas as neoplasias intracranianas.<\/li>\n<li><strong>Idade:<\/strong> A maior incid\u00eancia ocorre nos tr\u00eas primeiros anos de vida.<\/li>\n<li><strong>Localiza\u00e7\u00e3o:<\/strong> Em crian\u00e7as, o tumor geralmente est\u00e1 localizado nos ventr\u00edculos laterais, enquanto em adultos, localiza-se principalmente no quarto ventr\u00edculo. A propor\u00e7\u00e3o entre os sexos \u00e9 aproximadamente igual.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"manifestacoes-clinicas-e-sintomas-de-tumor-do-plexo-coroide\"><strong>Manifesta\u00e7\u00f5es cl\u00ednicas e sintomas de tumor do plexo coroide<\/strong><\/h2>\n<p>O principal sintoma \u00e9 a hipertens\u00e3o intracraniana devido \u00e0 hidrocefalia (excesso de produ\u00e7\u00e3o de liquor). Manifesta-se como dor de cabe\u00e7a, e em beb\u00eas como aumento da cabe\u00e7a.<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Outras manifesta\u00e7\u00f5es:<\/strong> n\u00e1usea, v\u00f4mitos, c\u00e2imbra, hemiparesia, letargia, defici\u00eancia visual (dependendo da localiza\u00e7\u00e3o).<\/li>\n<li>Em alguns casos, pode ocorrer hemorragia intracraniana.<\/li>\n<\/ul>\n<figure class=\"wp-block-video\" id=\"animacao-3d-papiloma-do-plexo-coroide\"><video controls><source data-src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webm\" type=\"video\/webm\"><\/source><\/video><figcaption class=\"wp-element-caption\">Anima\u00e7\u00e3o 3D \u2013 papiloma do plexo coroide<\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"classificacao-de-tumores-do-plexo-coroide\"><strong>Classifica\u00e7\u00e3o de tumores do plexo coroide<\/strong><\/h2>\n<p>A classifica\u00e7\u00e3o moderna (OMS, 5\u00aa edi\u00e7\u00e3o, 2021) baseia-se nas caracter\u00edsticas morfol\u00f3gicas, imuno-histoqu\u00edmicas e moleculares.<\/p>\n<h3 class=\"wp-block-heading\" id=\"who-grade-grau-de-malignidade\"><strong>WHO Grade (Grau de malignidade)<\/strong><\/h3>\n<figure class=\"wp-block-table table-to-cards\">\n<table class=\"has-fixed-layout\">\n<thead>\n<tr>\n<th class=\"has-text-align-center\" data-align=\"center\"><strong>WHO Grade<\/strong><\/th>\n<th class=\"has-text-align-center\" data-align=\"center\"><strong>Nome<\/strong><\/th>\n<th class=\"has-text-align-center\" data-align=\"center\"><strong>Caracter\u00edsticas<\/strong><\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Grade 1<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Papiloma do plexo caroide<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\">Forma benigna<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Grade 2<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>PPC at\u00edpico (aPPC)<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\">\u00c9 caracterizado por aumento da atividade mit\u00f3tica; maior risco de recorr\u00eancia.<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Grade 3<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>\u0421arcinoma do plexo caroide (CPC)<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\">Maligno, invasivo<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<\/figure>\n<h3 class=\"wp-block-heading\" id=\"classificacao-molecular\"><strong>Classifica\u00e7\u00e3o molecular <\/strong><\/h3>\n<p>Estudos modernos distinguem tr\u00eas subtipos moleculares, definidos pela metila\u00e7\u00e3o e pela express\u00e3o de genes:<\/p>\n<ol class=\"wp-block-list\">\n<li>Tumor supratentorial pedi\u00e1trico de baixo risco do plexo coroide (<strong>PPC\/aPPC<\/strong>)<\/li>\n<li>Tumor supratentorial pedi\u00e1trico de alto risco do plexo coroide (<strong>CPC<\/strong>)<\/li>\n<li>Tumor infratentorial adulto de baixo risco do plexo coroide (<strong>PSS\/aPSS<\/strong>)<\/li>\n<\/ol>\n<p>Assim, na pr\u00e1tica cl\u00ednica moderna, s\u00e3o levados em considera\u00e7\u00e3o a morfologia, a atividade proliferativa, os marcadores moleculares e o status do TP53<strong>,<\/strong> determinando o progn\u00f3stico e a extens\u00e3o da terapia.<\/p>\n<h2 class=\"wp-block-heading\" id=\"diagnostico-medico-e-diagnostico-diferencial\"><strong>Diagn\u00f3stico m\u00e9dico e diagn\u00f3stico diferencial<\/strong><\/h2>\n<h3 class=\"wp-block-heading\" id=\"metodos-de-diagnostico\"><strong>M\u00e9todos de diagn\u00f3stico<\/strong><\/h3>\n<p>O principal m\u00e9todo \u00e9 a resson\u00e2ncia magn\u00e9tica (RM). Caso realizar esse m\u00e9todo seja imposs\u00edvel, \u00e9 utilizada a tomografia computadorizada ou o ultrassom (na primeira inf\u00e2ncia, por meio da fontanela).<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>RM e TC:<\/strong> Um tumor do plexo coroide geralmente apresenta hipersinal em T2, na maioria das vezes cont\u00e9m \u00e1reas de calcifica\u00e7\u00e3o na TC e, al\u00e9m disso, mostra maior capta\u00e7\u00e3o de contraste.<\/li>\n<\/ul>\n<p><strong>O CPC<\/strong>\u00e9 caracterizado pela heterogeneidade estrutural, pelas \u00e1reas de necrose, invas\u00e3o, pelo aumento do contraste e pelos sinais de edema vasog\u00eanico ao redor do tumor.<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Diagn\u00f3stico molecular:<\/strong> O rastreio da s\u00edndrome de Li-Fraumeni (TP53 germline) \u00e9 obrigat\u00f3rio em todos os casos do CPC.<\/li>\n<li><strong>Pun\u00e7\u00e3o lombar:<\/strong>\u00c9 realizada para excluir c\u00e9lulas tumorais no l\u00edquor (na CPC).<\/li>\n<\/ul>\n<h3 class=\"wp-block-heading\" id=\"diagnostico-diferencial\"><strong>Diagn\u00f3stico diferencial<\/strong><\/h3>\n<figure class=\"wp-block-table table-to-cards\">\n<table class=\"has-fixed-layout\">\n<thead>\n<tr>\n<th class=\"has-text-align-center\" data-align=\"center\"><strong>Tipo de tumor<\/strong><\/th>\n<th class=\"has-text-align-center\" data-align=\"center\"><strong>Em crian\u00e7as (exemplos)<\/strong><\/th>\n<th class=\"has-text-align-center\" data-align=\"center\"><strong>Em adultos (exemplos)<\/strong><\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>PPC\/aPPC<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\">Ependimoma, Meduloblastoma, Astrocitoma piloc\u00edtico<\/td>\n<td class=\"has-text-align-center\" data-align=\"center\">Meningioma papilar, Adenocarcinoma metast\u00e1tico, Tumor fibroso solit\u00e1rio<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>CPC<\/strong><\/td>\n<td class=\"has-text-align-center\" data-align=\"center\">Tumor teratoide rabdoide at\u00edpico (ATRT), Tumor embrion\u00e1rio (ETMR), Ependimoma, Met\u00e1stases (raras)<\/td>\n<td class=\"has-text-align-center\" data-align=\"center\">Met\u00e1stases, Coriocarcinoma, Meningioma papilar de alto grau<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<\/figure>\n<p>Ent\u00e3o, em crian\u00e7as, o diagn\u00f3stico diferencial concentra-se em ependimomas e tumores embrion\u00e1rios, e em adultos, em meningiomas e carcinomas metast\u00e1ticos.<\/p>\n<div class=\"social-banner-block\">\n<div class=\"social-banner-content\">\n<p class=\"h5-title text-black\">Encontra mais conte\u00fados cientificamente exactos nas nossas redes sociais<\/p>\n<p><span class=\"social-banner-text text-grey\">Subscreve e n\u00e3o percas os recursos mais recentes<\/span><\/p>\n<div class=\"social-links-wrapper\"><a class=\"social-icon-link\" href=\"https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/facebook.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.instagram.com\/voka.io\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/insta.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.linkedin.com\/company\/voka-io\/posts\/?feedView=all\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/linkedin.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.youtube.com\/@vokaio\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/youtube.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.pinterest.com\/voka3danatomyandpathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/pinterest.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.tiktok.com\/@voka.io\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/tiktok.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/discord.gg\/7ejUpq8DRR\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/discord.svg\" alt=\"social link\"><\/a><\/div>\n<\/div>\n<p><img decoding=\"async\" class=\"social-banner-image\" loading=\"lazy\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/social-media-banner-mobile-image.webp\" alt=\"Banner background\"><\/div>\n<h2 class=\"wp-block-heading\" id=\"metodos-de-tratamento-e-estrategias-de-prognostico-no-tumor-do-plexo-coroide\"><strong>M\u00e9todos de tratamento e estrat\u00e9gias de progn\u00f3stico no tumor do plexo coroide<\/strong><\/h2>\n<p>O tratamento do tumor \u00e9 multimodal e come\u00e7a com a cirurgia, determinando as t\u00e1ticas subsequentes e o progn\u00f3stico.<\/p>\n<h3 class=\"wp-block-heading\" id=\"1-tratamento-cirurgico\">1. <strong>Tratamento cir\u00fargico<\/strong><\/h3>\n<ul class=\"wp-block-list\">\n<li><strong>Padr\u00e3o ouro:<\/strong><strong>Remo\u00e7\u00e3o total (gross total)<\/strong>. T\u00e9cnicas endosc\u00f3picas s\u00e3o utilizadas com frequ\u00eancia.<\/li>\n<li><strong>Progn\u00f3stico para o PPC:<\/strong> Geralmente, mesmo a ressec\u00e7\u00e3o subtotal no PPC cl\u00e1ssico proporciona um progn\u00f3stico favor\u00e1vel.<\/li>\n<li><strong>Complica\u00e7\u00f5es do PSS:<\/strong> A remo\u00e7\u00e3o completa \u00e9 frequentemente dif\u00edcil devido \u00e0 invas\u00e3o e ao sangramento intraoperat\u00f3rio.<\/li>\n<li><strong>P\u00f3s-operat\u00f3rio:<\/strong> Pode ser necess\u00e1rio o bypass devido \u00e0 disfun\u00e7\u00e3o do l\u00edquor.<\/li>\n<\/ul>\n<h3 class=\"wp-block-heading\" id=\"2-radioterapia\">2. <strong>Radioterapia<\/strong><\/h3>\n<ul class=\"wp-block-list\">\n<li><strong>PPC:<\/strong> Normalmente, ap\u00f3s a ressec\u00e7\u00e3o radical n\u00e3o \u00e9 necess\u00e1ria.<\/li>\n<li><strong>Indica\u00e7\u00f5es:<\/strong> \u00c9 realizada ap\u00f3s recidivas repetidas, quando a ressec\u00e7\u00e3o adequada \u00e9 imposs\u00edvel ou nas formas at\u00edpicas.<\/li>\n<li><strong>CPC:<\/strong> Pacientes com mais de 3 anos ap\u00f3s a quimioterapia recebem a irradia\u00e7\u00e3o cranioespinhal.<\/li>\n<li><strong>Limita\u00e7\u00f5es:<\/strong> Em crian\u00e7as de primeira linha, o procedimento \u00e9 evitado devido ao risco de comprometimento cognitivo. Em crian\u00e7as < com 3 anos de idade e em pacientes com a s\u00edndrome de Li-Fraumeni, o procedimento deve ser utilizado com extrema cautela devido ao risco de tumores secund\u00e1rios.<\/li>\n<\/ul>\n<h3 class=\"wp-block-heading\" id=\"3-quimioterapia\">3. <strong>Quimioterapia<\/strong><\/h3>\n<ul class=\"wp-block-list\">\n<li><strong>\u00c9 utilizada:<\/strong> Para pacientes de alto risco (CPC, aPPC com tumor residual, met\u00e1stases).<\/li>\n<li><strong>Regimes principais:<\/strong> Carboplatin\/Etoposide\/Vincristine (CarbEV); CycEV. No CPC, o CarbEV \u00e9 mais eficaz em termos de sobrevida no CPC.<\/li>\n<li>Em alguns casos, na s\u00edndrome de Li-Fraumeni, \u00e9 utilizada a quimioterapia de consolida\u00e7\u00e3o em altas doses com transplante aut\u00f3logo da medula \u00f3ssea.<\/li>\n<\/ul>\n<h3 class=\"wp-block-heading\" id=\"prognostico-e-fatores-de-sobrevida\"><strong>Progn\u00f3stico e fatores de sobrevida<\/strong><\/h3>\n<ul class=\"wp-block-list\">\n<li><strong>Favor\u00e1vel:<\/strong> Ap\u00f3s a remo\u00e7\u00e3o completa do PPC\/aPPC , a taxa de sobrevida em 10 anos \u00e9 mais de 90%. Para o aPPC , o risco de recorr\u00eancia \u00e9 maior; na maioria dos casos, \u00e9 necess\u00e1ria a terapia adjuvante (p\u00f3s-operat\u00f3ria).<\/li>\n<li><strong>Desfavor\u00e1vel:<\/strong> O progn\u00f3stico para o CPC \u00e9 pior (sobrevida em 5 anos de at\u00e9 40%) na presen\u00e7a de muta\u00e7\u00e3o do TP53. O progn\u00f3stico piora na presen\u00e7a de s\u00edndromes gen\u00e9ticas, met\u00e1stases, ressec\u00e7\u00e3o incompleta e em pacientes com a s\u00edndrome de Li-Fraumeni.<\/li>\n<\/ul>\n<div>\n<h2 class=\"faq-title h2-article\" id=\"faq\">FAQ<\/h2>\n<div class=\"faq-section\">\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">1. Qual \u00e9 a diferen\u00e7a entre o papiloma do plexo coroide e o carcinoma?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">O papiloma (PPC) \u00e9 um tumor benigno (WHO Grade 1) com progn\u00f3stico favor\u00e1vel, enquanto o carcinoma (CPC) \u00e9 um tumor altamente maligno (WHO Grade 3) com curso agressivo e progn\u00f3stico pior.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">2. Qual \u00e9 o principal sintoma do tumor do plexo coroide?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">O principal sintoma \u00e9 a hipertens\u00e3o intracraniana causada pelo aumento da produ\u00e7\u00e3o de l\u00edquor (hidrocefalia). Em lactentes, isso geralmente se manifesta como aumento da cabe\u00e7a.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">3. Qual \u00e9 o papel da muta\u00e7\u00e3o do TP53 no diagn\u00f3stico do CPC? <\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">A muta\u00e7\u00e3o do TP53 tem importante significado progn\u00f3stico: ela est\u00e1 frequentemente associada \u00e0 s\u00edndrome de Li-Fraumeni e indica um pior progn\u00f3stico no carcinoma do plexo coroide.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">4. Qual tratamento \u00e9 considerado o padr\u00e3o ouro para o PPC?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">O tratamento padr\u00e3o-ouro para o papiloma do plexo coroide (PPC) \u00e9 a remo\u00e7\u00e3o cir\u00fargica total do tumor (Gross Total Resection).<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">5. Por que a radioterapia \u00e9 evitada no tratamento do PPC em crian\u00e7as pequenas?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">A radioterapia \u00e9 evitada em crian\u00e7as menores de 3 anos de idade devido ao alto risco de comprometimento cognitivo grave e tamb\u00e9m devido ao risco de tumores secund\u00e1rios, especialmente em pacientes com a s\u00edndrome de Li-Fraumeni.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"sources-list-block sources-list-hidden\" id=\"referencias\">\n<div class=\"sources-list-content\">\n<div class=\"sources-list-title\">\n<p class=\"small-text-bold text-black sources-list-title-text\">Refer\u00eancias<\/p>\n<div class=\"sources-expand-button-wrapper-mobile\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n<div class=\"sources-list-items\">\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">1.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Cat\u00e1logo VOKA. [Recurso eletr\u00f4nico]<\/cite><\/p>\n<p><span class=\"small-text-medium text-grey\">https:\/\/catalog.voka.io\/<\/span><\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">2.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Wolff JE, et al. \u201cFinal results of the Choroid Plexus Tumor study CPT-SIOP-2000.\u201d J Neurooncol 2022;156(3):599\u2013613. <\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">3.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Louis DN, et al. \u201cThe 2021 WHO Classification of Tumors of the Central Nervous System: a summary.\u201d Neuro Oncol. 2021;23:1231\u20131251.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">4.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Thomas C, et al. \u201cMolecular genetics and diversity of choroid plexus tumors.\u201d Neuro-Oncol Adv 2024.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">5.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Andour H, et al. \u201cAtypical choroid plexus papilloma: Diagnosis and management.\u201d SAGE Open Med. 2024; doi:10.1177\/2050313X241254000.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">6.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Yankelevich M, et al. \u201cMarrow-ablative consolidation chemotherapy and molecular targeted therapy for CPC.\u201d Neuro-Oncol Adv 2024;6(1):vdae109.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">7.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Cornelius A, et al.  \u201cMolecular Guided Therapy Provides Sustained Clinical Remission in Pediatric CPC.\u201d Frontiers Pharmacol. 2017;8:652.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">8.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Wolff JE, Sajedi M, Brant R. \u201cChoroid plexus tumours.\u201d Br J Cancer. 2002 87:1086\u201391.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">9.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Safaee M, et al. \u201cChoroid plexus papillomas: advances in molecular biology and surgical management.\u201d Neurosurg Focus. 2012;32(2):E6.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">10.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Akade E, et al. \u201cDiagnosis of choroid plexus papilloma.\u201d Curr Probl Cancer. 2024; doi:10.1016\/j.cpt.2023.09.005.<\/cite><\/p>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"sources-expand-button-wrapper\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>O plexo coroide produz o l\u00edquor (l\u00edquido cefalorraquidiano) e est\u00e1 localizado nos ventr\u00edculos cerebrais. A localiza\u00e7\u00e3o do tumor depende da idade: em crian\u00e7as, os ventr\u00edculos laterais s\u00e3o afetados com mais frequ\u00eancia, enquanto em adultos, o \u00f3rg\u00e3o mais afetado \u00e9 o quarto ventr\u00edculo. O papiloma do plexo coroide (PPC) \u00e9 um tumor benigno do epit\u00e9lio do [&hellip;]<\/p>\n","protected":false},"author":11,"featured_media":0,"template":"","diseases_category":[352],"class_list":["post-2010","diseases_post","type-diseases_post","status-publish","hentry","diseases_category-oncologia"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v25.0 (Yoast SEO v26.5) - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Tumores do plexo coroide: papiloma e carcinoma \u2013 diagn\u00f3stico e tratamento<\/title>\n<meta name=\"description\" content=\"Um guia completo sobre tumores do plexo coroide (PPC e CPC): etiologia, sintomas, classifica\u00e7\u00e3o WHO, diagn\u00f3stico molecular e m\u00e9todos de tratamento.\" \/>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"pt_PT\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Tumores do plexo coroide: papiloma e carcinoma \u2013 etiologia, classifica\u00e7\u00e3o e tratamento\" \/>\n<meta property=\"og:description\" content=\"Um guia completo sobre tumores do plexo coroide (PPC e CPC): etiologia, sintomas, classifica\u00e7\u00e3o WHO, diagn\u00f3stico molecular e m\u00e9todos de tratamento.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/\" \/>\n<meta property=\"og:site_name\" content=\"Voka Wiki\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/\" \/>\n<meta property=\"article:modified_time\" content=\"2025-12-11T12:05:55+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Tempo estimado de leitura\" \/>\n\t<meta name=\"twitter:data1\" content=\"6 minutos\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#article\",\"isPartOf\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/\"},\"author\":{\"name\":\"Artemiy G.\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/person\/ab068df9b8f89e81a4974c8fc3697690\"},\"headline\":\"Tumores do plexo coroide: papiloma e carcinoma \u2013 etiologia, classifica\u00e7\u00e3o e tratamento\",\"datePublished\":\"2025-12-11T12:05:48+00:00\",\"dateModified\":\"2025-12-11T12:05:55+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/\"},\"wordCount\":1204,\"publisher\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#organization\"},\"image\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage\"},\"thumbnailUrl\":\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp\",\"inLanguage\":\"pt-PT\"},{\"@type\":\"WebPage\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/\",\"url\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/\",\"name\":\"Tumores do plexo coroide: papiloma e carcinoma \u2013 diagn\u00f3stico e tratamento\",\"isPartOf\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage\"},\"image\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage\"},\"thumbnailUrl\":\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp\",\"datePublished\":\"2025-12-11T12:05:48+00:00\",\"dateModified\":\"2025-12-11T12:05:55+00:00\",\"description\":\"Um guia completo sobre tumores do plexo coroide (PPC e CPC): etiologia, sintomas, classifica\u00e7\u00e3o WHO, diagn\u00f3stico molecular e m\u00e9todos de tratamento.\",\"breadcrumb\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#breadcrumb\"},\"inLanguage\":\"pt-PT\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/\"]}]},{\"@type\":\"ImageObject\",\"inLanguage\":\"pt-PT\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage\",\"url\":\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp\",\"contentUrl\":\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp\"},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/wiki.dev.voka.io\/pt\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Oncologia\",\"item\":\"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Tumores do plexo coroide: papiloma e carcinoma \u2013 etiologia, classifica\u00e7\u00e3o e tratamento\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#website\",\"url\":\"https:\/\/wiki.dev.voka.io\/pt\/\",\"name\":\"Voka Wiki\",\"description\":\"\",\"publisher\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#organization\"},\"alternateName\":\"Anatomy & Pathology Wiki by VOKA\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/wiki.dev.voka.io\/pt\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"pt-PT\"},{\"@type\":\"Organization\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#organization\",\"name\":\"Voka 3D Anatomy & Pathology\",\"alternateName\":\"VOKA\",\"url\":\"https:\/\/wiki.dev.voka.io\/pt\/\",\"logo\":{\"@type\":\"ImageObject\",\"inLanguage\":\"pt-PT\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/logo\/image\/\",\"url\":\"https:\/\/wiki.dev.voka.io\/wp-content\/uploads\/2025\/02\/cropped-voka-logo-1.png\",\"contentUrl\":\"https:\/\/wiki.dev.voka.io\/wp-content\/uploads\/2025\/02\/cropped-voka-logo-1.png\",\"width\":70,\"height\":16,\"caption\":\"Voka 3D Anatomy & Pathology\"},\"image\":{\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/logo\/image\/\"},\"sameAs\":[\"https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/\",\"https:\/\/www.instagram.com\/voka.io\/\",\"https:\/\/www.linkedin.com\/company\/voka-io\/\",\"https:\/\/www.youtube.com\/channel\/UCqGGuOEpr62ScH8Pjk2q5zw\/videos\",\"https:\/\/www.pinterest.com\/VokaAnatomyPro\/\",\"https:\/\/www.threads.com\/@voka.io\"],\"description\":\"VOKA.io offers 3D medical animations and custom 3D modeling services. Our product, VOKA 3D Anatomy & Pathology, is a digital atlas with over 1,000 detailed 3D models of human anatomy and pathology, designed for medical education, training, and patient communication.\",\"email\":\"info@voka.io\",\"telephone\":\"+1 814 351 4442\",\"legalName\":\"Voka 3D Anatomy & Pathology\",\"foundingDate\":\"2017-02-12\",\"naics\":\"541512\",\"numberOfEmployees\":{\"@type\":\"QuantitativeValue\",\"minValue\":\"51\",\"maxValue\":\"200\"},\"publishingPrinciples\":\"https:\/\/wiki.voka.io\/pt\/principios-de-publicacao\/\"},{\"@type\":\"Person\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/person\/ab068df9b8f89e81a4974c8fc3697690\",\"name\":\"Artemiy G.\",\"image\":{\"@type\":\"ImageObject\",\"inLanguage\":\"pt-PT\",\"@id\":\"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/person\/image\/\",\"url\":\"https:\/\/secure.gravatar.com\/avatar\/41c2ff0508515a8e31a999a47b4643f8332f73d15d3a8e06b016e20b8327c52d?s=96&d=mm&r=g\",\"contentUrl\":\"https:\/\/secure.gravatar.com\/avatar\/41c2ff0508515a8e31a999a47b4643f8332f73d15d3a8e06b016e20b8327c52d?s=96&d=mm&r=g\",\"caption\":\"Artemiy G.\"}}]}<\/script>\n<!-- \/ Yoast SEO Premium plugin. -->","yoast_head_json":{"title":"Tumores do plexo coroide: papiloma e carcinoma \u2013 diagn\u00f3stico e tratamento","description":"Um guia completo sobre tumores do plexo coroide (PPC e CPC): etiologia, sintomas, classifica\u00e7\u00e3o WHO, diagn\u00f3stico molecular e m\u00e9todos de tratamento.","robots":{"index":"noindex","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"og_locale":"pt_PT","og_type":"article","og_title":"Tumores do plexo coroide: papiloma e carcinoma \u2013 etiologia, classifica\u00e7\u00e3o e tratamento","og_description":"Um guia completo sobre tumores do plexo coroide (PPC e CPC): etiologia, sintomas, classifica\u00e7\u00e3o WHO, diagn\u00f3stico molecular e m\u00e9todos de tratamento.","og_url":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/","og_site_name":"Voka Wiki","article_publisher":"https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/","article_modified_time":"2025-12-11T12:05:55+00:00","og_image":[{"url":"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp","type":"","width":"","height":""}],"twitter_card":"summary_large_image","twitter_misc":{"Tempo estimado de leitura":"6 minutos"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"Article","@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#article","isPartOf":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/"},"author":{"name":"Artemiy G.","@id":"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/person\/ab068df9b8f89e81a4974c8fc3697690"},"headline":"Tumores do plexo coroide: papiloma e carcinoma \u2013 etiologia, classifica\u00e7\u00e3o e tratamento","datePublished":"2025-12-11T12:05:48+00:00","dateModified":"2025-12-11T12:05:55+00:00","mainEntityOfPage":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/"},"wordCount":1204,"publisher":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/#organization"},"image":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage"},"thumbnailUrl":"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp","inLanguage":"pt-PT"},{"@type":"WebPage","@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/","url":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/","name":"Tumores do plexo coroide: papiloma e carcinoma \u2013 diagn\u00f3stico e tratamento","isPartOf":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/#website"},"primaryImageOfPage":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage"},"image":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage"},"thumbnailUrl":"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp","datePublished":"2025-12-11T12:05:48+00:00","dateModified":"2025-12-11T12:05:55+00:00","description":"Um guia completo sobre tumores do plexo coroide (PPC e CPC): etiologia, sintomas, classifica\u00e7\u00e3o WHO, diagn\u00f3stico molecular e m\u00e9todos de tratamento.","breadcrumb":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#breadcrumb"},"inLanguage":"pt-PT","potentialAction":[{"@type":"ReadAction","target":["https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/"]}]},{"@type":"ImageObject","inLanguage":"pt-PT","@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#primaryimage","url":"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp","contentUrl":"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/oncology\/choroid-plexus-tumors\/choroid-plexus-papilloma.webp"},{"@type":"BreadcrumbList","@id":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/tumores-do-plexo-coroide\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Home","item":"https:\/\/wiki.dev.voka.io\/pt\/"},{"@type":"ListItem","position":2,"name":"Oncologia","item":"https:\/\/wiki.dev.voka.io\/pt\/doencas\/oncologia\/"},{"@type":"ListItem","position":3,"name":"Tumores do plexo coroide: papiloma e carcinoma \u2013 etiologia, classifica\u00e7\u00e3o e tratamento"}]},{"@type":"WebSite","@id":"https:\/\/wiki.dev.voka.io\/pt\/#website","url":"https:\/\/wiki.dev.voka.io\/pt\/","name":"Voka Wiki","description":"","publisher":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/#organization"},"alternateName":"Anatomy & Pathology Wiki by VOKA","potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/wiki.dev.voka.io\/pt\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"pt-PT"},{"@type":"Organization","@id":"https:\/\/wiki.dev.voka.io\/pt\/#organization","name":"Voka 3D Anatomy & Pathology","alternateName":"VOKA","url":"https:\/\/wiki.dev.voka.io\/pt\/","logo":{"@type":"ImageObject","inLanguage":"pt-PT","@id":"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/logo\/image\/","url":"https:\/\/wiki.dev.voka.io\/wp-content\/uploads\/2025\/02\/cropped-voka-logo-1.png","contentUrl":"https:\/\/wiki.dev.voka.io\/wp-content\/uploads\/2025\/02\/cropped-voka-logo-1.png","width":70,"height":16,"caption":"Voka 3D Anatomy & Pathology"},"image":{"@id":"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/logo\/image\/"},"sameAs":["https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/","https:\/\/www.instagram.com\/voka.io\/","https:\/\/www.linkedin.com\/company\/voka-io\/","https:\/\/www.youtube.com\/channel\/UCqGGuOEpr62ScH8Pjk2q5zw\/videos","https:\/\/www.pinterest.com\/VokaAnatomyPro\/","https:\/\/www.threads.com\/@voka.io"],"description":"VOKA.io offers 3D medical animations and custom 3D modeling services. Our product, VOKA 3D Anatomy & Pathology, is a digital atlas with over 1,000 detailed 3D models of human anatomy and pathology, designed for medical education, training, and patient communication.","email":"info@voka.io","telephone":"+1 814 351 4442","legalName":"Voka 3D Anatomy & Pathology","foundingDate":"2017-02-12","naics":"541512","numberOfEmployees":{"@type":"QuantitativeValue","minValue":"51","maxValue":"200"},"publishingPrinciples":"https:\/\/wiki.voka.io\/pt\/principios-de-publicacao\/"},{"@type":"Person","@id":"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/person\/ab068df9b8f89e81a4974c8fc3697690","name":"Artemiy G.","image":{"@type":"ImageObject","inLanguage":"pt-PT","@id":"https:\/\/wiki.dev.voka.io\/pt\/#\/schema\/person\/image\/","url":"https:\/\/secure.gravatar.com\/avatar\/41c2ff0508515a8e31a999a47b4643f8332f73d15d3a8e06b016e20b8327c52d?s=96&d=mm&r=g","contentUrl":"https:\/\/secure.gravatar.com\/avatar\/41c2ff0508515a8e31a999a47b4643f8332f73d15d3a8e06b016e20b8327c52d?s=96&d=mm&r=g","caption":"Artemiy G."}}]}},"_links":{"self":[{"href":"https:\/\/wiki.dev.voka.io\/pt\/wp-json\/wp\/v2\/diseases_post\/2010","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/wiki.dev.voka.io\/pt\/wp-json\/wp\/v2\/diseases_post"}],"about":[{"href":"https:\/\/wiki.dev.voka.io\/pt\/wp-json\/wp\/v2\/types\/diseases_post"}],"author":[{"embeddable":true,"href":"https:\/\/wiki.dev.voka.io\/pt\/wp-json\/wp\/v2\/users\/11"}],"wp:attachment":[{"href":"https:\/\/wiki.dev.voka.io\/pt\/wp-json\/wp\/v2\/media?parent=2010"}],"wp:term":[{"taxonomy":"diseases_category","embeddable":true,"href":"https:\/\/wiki.dev.voka.io\/pt\/wp-json\/wp\/v2\/diseases_category?post=2010"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}