{"id":554,"date":"2025-05-07T12:48:33","date_gmt":"2025-05-07T09:48:33","guid":{"rendered":"https:\/\/wiki.dev.voka.io\/diseases\/uncategorized\/paragangliom\/"},"modified":"2026-04-24T10:28:45","modified_gmt":"2026-04-24T07:28:45","slug":"paragangliom","status":"publish","type":"diseases_post","link":"https:\/\/wiki.dev.voka.io\/de\/krankheit\/gefaesssystem\/paragangliom\/","title":{"rendered":"Glomus-caroticum-Paragangliom (Glomustumor der Carotis): \u00c4tiologie, Pathogenese, Klassifikation, Diagnostik, Behandlungsmethoden"},"content":{"rendered":"<p><?xml encoding=\"UTF-8\" ?><\/p>\n<p>\u041f\u0430\u0440\u0430\u0433\u0430\u043d\u0433\u043b\u0438\u043e\u043c\u0430 \u043a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u043e\u0433\u043e \u0442\u0435\u043b\u044c\u0446\u0430 (\u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430) \u2014 \u0440\u0435\u0434\u043a\u0430\u044f, \u043f\u0440\u0435\u0438\u043c\u0443\u0449\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u043e \u0434\u043e\u0431\u0440\u043e\u043a\u0430\u0447\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u0430\u044f \u043e\u043f\u0443\u0445\u043e\u043b\u044c, \u0432\u043e\u0437\u043d\u0438\u043a\u0430\u044e\u0449\u0430\u044f \u0438\u0437 \u0445\u0435\u043c\u043e\u0440\u0435\u0446\u0435\u043f\u0442\u043e\u0440\u043d\u044b\u0445 \u043a\u043b\u0435\u0442\u043e\u043a \u043a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u043e\u0433\u043e \u0442\u0435\u043b\u0430, \u0440\u0430\u0441\u043f\u043e\u043b\u043e\u0436\u0435\u043d\u043d\u043e\u0433\u043e \u0432 \u043c\u0435\u0441\u0442\u0435 \u0431\u0438\u0444\u0443\u0440\u043a\u0430\u0446\u0438\u0438 \u043e\u0431\u0449\u0435\u0439 \u0441\u043e\u043d\u043d\u043e\u0439 \u0430\u0440\u0442\u0435\u0440\u0438\u0438.<\/p>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/vascular-system\/paraganglioma\/chemodectoma-paraganglioma.webp\" alt=\"Glomus-caroticum-Paragangliom (Glomustumor der Carotis)\"><figcaption class=\"wp-element-caption\">\u0425\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 (\u043f\u0430\u0440\u0430\u0433\u0430\u043d\u0433\u043b\u0438\u043e\u043c\u0430) \u2013 <a href=\"https:\/\/catalog.voka.io\/ru\/models\/6e2f9dc5-6e91-46c4-b881-b038f53acd05\/6ec65686-8390-42c1-b3f3-c7a1f7148948\/aa66bddd-72b2-4945-91b8-90210e91fc55\/9db48cfc-4d8c-4de0-8e9c-e20a7d131626\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">3D-\u043c\u043e\u0434\u0435\u043b\u044c<\/a><\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"epidemiologie\">Epidemiologie <\/h2>\n<ul class=\"wp-block-list\">\n<li>Ungef\u00e4hr 1\u20132 F\u00e4lle pro 100.000 Einwohner.<\/li>\n<li>Frauen sind h\u00e4ufiger betroffen als M\u00e4nner. \u200b<\/li>\n<li>Das Durchschnittsalter bei der Diagnosestellung liegt bei etwa 45 Jahren.<\/li>\n<li>\u0412\u044b\u0441\u043e\u043a\u0430\u044f \u0440\u0430\u0441\u043f\u0440\u043e\u0441\u0442\u0440\u0430\u043d\u0435\u043d\u043d\u043e\u0441\u0442\u044c \u043e\u0442\u043c\u0435\u0447\u0430\u0435\u0442\u0441\u044f \u0432 \u0441\u0442\u0440\u0430\u043d\u0430\u0445 \u041b\u0430\u0442\u0438\u043d\u0441\u043a\u043e\u0439 \u0410\u043c\u0435\u0440\u0438\u043a\u0438, \u043e\u0441\u043e\u0431\u0435\u043d\u043d\u043e \u0432 \u041c\u0435\u043a\u0441\u0438\u043a\u0435, \u0433\u0434\u0435 \u0436\u0435\u043d\u0449\u0438\u043d\u044b \u0441\u043e\u0441\u0442\u0430\u0432\u043b\u044f\u044e\u0442 \u0434\u043e 90 % \u0441\u043b\u0443\u0447\u0430\u0435\u0432.<\/li>\n<li>Einwohner von Hochgebirgsregionen haben aufgrund des chronischen Sauerstoffmangels ein erh\u00f6htes Risiko, an Glomustumoren der Carotis zu erkranken.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"aetiologie\">\u00c4tiologie<\/h2>\n<p><strong>\u0413\u0435\u043d\u0435\u0442\u0438\u0447\u0435\u0441\u043a\u0438\u0435 \u043c\u0443\u0442\u0430\u0446\u0438\u0438<\/strong> \u2014 \u0432\u0435\u0434\u0443\u0449\u0443\u044e \u0440\u043e\u043b\u044c \u0438\u0433\u0440\u0430\u044e\u0442 \u043c\u0443\u0442\u0430\u0446\u0438\u0438 \u0432 \u0433\u0435\u043d\u0430\u0445, \u043a\u043e\u0434\u0438\u0440\u0443\u044e\u0449\u0438\u0445 \u0441\u0443\u0431\u044a\u0435\u0434\u0438\u043d\u0438\u0446\u044b \u0441\u0443\u043a\u0446\u0438\u043d\u0430\u0442\u0434\u0435\u0433\u0438\u0434\u0440\u043e\u0433\u0435\u043d\u0430\u0437\u043d\u043e\u0433\u043e \u043a\u043e\u043c\u043f\u043b\u0435\u043a\u0441\u0430 (SDH), \u043a\u043e\u0442\u043e\u0440\u044b\u0439 \u0443\u0447\u0430\u0441\u0442\u0432\u0443\u0435\u0442 \u0432 \u0434\u044b\u0445\u0430\u0442\u0435\u043b\u044c\u043d\u043e\u0439 \u0446\u0435\u043f\u0438 \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0439 \u0438 \u043a\u043b\u0435\u0442\u043e\u0447\u043d\u043e\u043c \u043c\u0435\u0442\u0430\u0431\u043e\u043b\u0438\u0437\u043c\u0435. \u041e\u0441\u043d\u043e\u0432\u043d\u044b\u0435 \u0433\u0435\u043d\u044b:<\/p>\n<ul class=\"wp-block-list\">\n<li><strong><em>SDHD<\/em><\/strong> \u2014 \u043d\u0430\u0438\u0431\u043e\u043b\u0435\u0435 \u0447\u0430\u0441\u0442\u043e \u0430\u0441\u0441\u043e\u0446\u0438\u0438\u0440\u043e\u0432\u0430\u043d \u0441 \u043c\u043d\u043e\u0436\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u044b\u043c\u0438 \u043f\u0430\u0440\u0430\u0433\u0430\u043d\u0433\u043b\u0438\u043e\u043c\u0430\u043c\u0438 \u0433\u043e\u043b\u043e\u0432\u044b \u0438 \u0448\u0435\u0438; \u043f\u0435\u0440\u0435\u0434\u0430\u0435\u0442\u0441\u044f \u043f\u043e \u043e\u0442\u0446\u043e\u0432\u0441\u043a\u043e\u0439 \u043b\u0438\u043d\u0438\u0438;<\/li>\n<li><strong><em>SDHB<\/em><\/strong> \u2014 \u0430\u0441\u0441\u043e\u0446\u0438\u0438\u0440\u043e\u0432\u0430\u043d \u0441 \u0431\u043e\u043b\u0435\u0435 \u0430\u0433\u0440\u0435\u0441\u0441\u0438\u0432\u043d\u044b\u043c\u0438 \u0444\u043e\u0440\u043c\u0430\u043c\u0438 \u0438 \u043f\u043e\u0432\u044b\u0448\u0435\u043d\u043d\u044b\u043c \u0440\u0438\u0441\u043a\u043e\u043c \u0437\u043b\u043e\u043a\u0430\u0447\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u043e\u0433\u043e \u0442\u0435\u0447\u0435\u043d\u0438\u044f;<\/li>\n<li><strong><em>SDHC<\/em><\/strong><strong>, <\/strong><strong><em>SDHA<\/em><\/strong><strong>, <\/strong><strong><em>SDHAF2<\/em><\/strong> \u2014 \u0440\u0435\u0436\u0435 \u0432\u043e\u0432\u043b\u0435\u0447\u0435\u043d\u044b, \u043d\u043e \u0442\u0430\u043a\u0436\u0435 \u043c\u043e\u0433\u0443\u0442 \u0441\u043f\u043e\u0441\u043e\u0431\u0441\u0442\u0432\u043e\u0432\u0430\u0442\u044c \u0440\u0430\u0437\u0432\u0438\u0442\u0438\u044e \u043e\u043f\u0443\u0445\u043e\u043b\u0438.<\/li>\n<\/ul>\n<p><strong>\u0421\u0438\u043d\u0434\u0440\u043e\u043c\u044b, <\/strong><strong>\u0430\u0441\u0441\u043e\u0446\u0438\u0438\u0440\u043e\u0432\u0430\u043d\u043d\u044b\u0435 \u0441 \u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430\u043c\u0438<\/strong>:\u00a0<\/p>\n<ul class=\"wp-block-list\">\n<li>\u0441\u0438\u043d\u0434\u0440\u043e\u043c \u0444\u043e\u043d \u0413\u0438\u043f\u043f\u0435\u043b\u044f \u2014 \u041b\u0438\u043d\u0434\u0430\u0443 (VHL);\u00a0<\/li>\n<li>\u043c\u043d\u043e\u0436\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u0430\u044f \u044d\u043d\u0434\u043e\u043a\u0440\u0438\u043d\u043d\u0430\u044f \u043d\u0435\u043e\u043f\u043b\u0430\u0437\u0438\u044f 2 \u0442\u0438\u043f\u0430 (MEN2);\u00a0<\/li>\n<li>\u043d\u0435\u0439\u0440\u043e\u0444\u0438\u0431\u0440\u043e\u043c\u0430\u0442\u043e\u0437 1 \u0442\u0438\u043f\u0430 (NF1)\u200b.<\/li>\n<\/ul>\n<p><strong>\u0425\u0440\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u0433\u0438\u043f\u043e\u043a\u0441\u0438\u044f<\/strong> \u2014 \u043f\u0440\u043e\u0436\u0438\u0432\u0430\u043d\u0438\u0435 \u043d\u0430 \u0432\u044b\u0441\u043e\u0442\u0435 \u0431\u043e\u043b\u0435\u0435 2000 \u043c \u043d\u0430\u0434 \u0443\u0440\u043e\u0432\u043d\u0435\u043c \u043c\u043e\u0440\u044f, \u0430 \u0442\u0430\u043a\u0436\u0435 \u0442\u0430\u043a\u0438\u0435 \u0441\u043e\u0441\u0442\u043e\u044f\u043d\u0438\u044f, \u043a\u0430\u043a \u0445\u0440\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u043e\u0431\u0441\u0442\u0440\u0443\u043a\u0442\u0438\u0432\u043d\u0430\u044f \u0431\u043e\u043b\u0435\u0437\u043d\u044c \u043b\u0435\u0433\u043a\u0438\u0445 \u0438 \u0432\u0440\u043e\u0436\u0434\u0435\u043d\u043d\u044b\u0435 \u043f\u043e\u0440\u043e\u043a\u0438 \u0441\u0435\u0440\u0434\u0446\u0430, \u043c\u043e\u0433\u0443\u0442 \u0441\u0442\u0438\u043c\u0443\u043b\u0438\u0440\u043e\u0432\u0430\u0442\u044c \u0433\u0438\u043f\u0435\u0440\u043f\u043b\u0430\u0437\u0438\u044e \u043a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u043e\u0433\u043e \u0442\u0435\u043b\u0430. \u200b<\/p>\n<p><strong>\u0421\u0435\u043c\u0435\u0439\u043d\u044b\u0439 \u0430\u043d\u0430\u043c\u043d\u0435\u0437 \u2014 \u043e\u043a\u043e\u043b\u043e 10\u00a0%<\/strong> \u0441\u043b\u0443\u0447\u0430\u0435\u0432 \u044f\u0432\u043b\u044f\u044e\u0442\u0441\u044f \u0441\u0435\u043c\u0435\u0439\u043d\u044b\u043c\u0438.<\/p>\n<div class=\"videos-carousel-block\">\n<div class=\"swiper video-carousel-swiper video-carousel-swiper-block_69ef7150e2c17\">\n<div class=\"swiper-wrapper\">\n<div class=\"swiper-slide\"><video controls class=\"carousel-video\"><source data-src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/%20Chemodectoma\/chemodectoma-type-1.webm\" type=\"video\/webm\"><\/source><\/video><span class=\"small-text-article text-main-text-color\">3D-\u0430\u043d\u0438\u043c\u0430\u0446\u0438\u044f \u2013 \u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 I \u0442\u0438\u043f<\/span><\/div>\n<div class=\"swiper-slide\"><video controls class=\"carousel-video\"><source data-src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/%20Chemodectoma\/chemodectoma-type-3.webm\" type=\"video\/webm\"><\/source><\/video><span class=\"small-text-article text-main-text-color\">3D-\u0430\u043d\u0438\u043c\u0430\u0446\u0438\u044f \u2013 \u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 III \u0442\u0438\u043f<\/span><\/div>\n<\/div>\n<\/div>\n<div class=\"swiper-article-video-carousel__controls\">\n<div class=\"swiper-article-video-carousel__pagination-container swiper-article-video-carousel__pagination-container-block_69ef7150e2c17\"><\/div>\n<div class=\"swiper-article-video-carousel__arrows\"><button class=\"swiper__arrow swiper__arrow--prev video-carousel-swiper-button-prev swiper__arrow swiper__arrow--prev video-carousel-swiper-button-prev-block_69ef7150e2c17\"><svg xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"40\" height=\"40\" viewbox=\"0 0 40 40\" fill=\"none\"><path d=\"M20 3.75C16.7861 3.75 13.6443 4.70305 10.972 6.48862C8.29969 8.27419 6.21689 10.8121 4.98696 13.7814C3.75704 16.7507 3.43524 20.018 4.06225 23.1702C4.68926 26.3224 6.23692 29.2179 8.50952 31.4905C10.7821 33.7631 13.6776 35.3107 16.8298 35.9378C19.982 36.5648 23.2493 36.243 26.2186 35.013C29.1879 33.7831 31.7258 31.7003 33.5114 29.028C35.297 26.3557 36.25 23.2139 36.25 20C36.2455 15.6916 34.5319 11.561 31.4855 8.51454C28.439 5.46806 24.3084 3.75455 20 3.75ZM23.3844 25.3656C23.5005 25.4818 23.5926 25.6196 23.6555 25.7714C23.7184 25.9231 23.7507 26.0858 23.7507 26.25C23.7507 26.4142 23.7184 26.5769 23.6555 26.7286C23.5926 26.8804 23.5005 27.0182 23.3844 27.1344C23.2682 27.2505 23.1304 27.3426 22.9786 27.4055C22.8269 27.4683 22.6643 27.5007 22.5 27.5007C22.3358 27.5007 22.1731 27.4683 22.0214 27.4055C21.8696 27.3426 21.7318 27.2505 21.6156 27.1344L15.3656 20.8844C15.2494 20.7683 15.1572 20.6304 15.0943 20.4787C15.0314 20.3269 14.999 20.1643 14.999 20C14.999 19.8357 15.0314 19.6731 15.0943 19.5213C15.1572 19.3696 15.2494 19.2317 15.3656 19.1156L21.6156 12.8656C21.7318 12.7495 21.8696 12.6574 22.0214 12.5945C22.1731 12.5317 22.3358 12.4993 22.5 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33.7831 31.7258 31.7003 33.5114 29.028C35.297 26.3557 36.25 23.2139 36.25 20C36.2455 15.6916 34.5319 11.561 31.4855 8.51454C28.439 5.46806 24.3084 3.75455 20 3.75ZM23.3844 25.3656C23.5005 25.4818 23.5926 25.6196 23.6555 25.7714C23.7184 25.9231 23.7507 26.0858 23.7507 26.25C23.7507 26.4142 23.7184 26.5769 23.6555 26.7286C23.5926 26.8804 23.5005 27.0182 23.3844 27.1344C23.2682 27.2505 23.1304 27.3426 22.9786 27.4055C22.8269 27.4683 22.6643 27.5007 22.5 27.5007C22.3358 27.5007 22.1731 27.4683 22.0214 27.4055C21.8696 27.3426 21.7318 27.2505 21.6156 27.1344L15.3656 20.8844C15.2494 20.7683 15.1572 20.6304 15.0943 20.4787C15.0314 20.3269 14.999 20.1643 14.999 20C14.999 19.8357 15.0314 19.6731 15.0943 19.5213C15.1572 19.3696 15.2494 19.2317 15.3656 19.1156L21.6156 12.8656C21.7318 12.7495 21.8696 12.6574 22.0214 12.5945C22.1731 12.5317 22.3358 12.4993 22.5 12.4993C22.6643 12.4993 22.8269 12.5317 22.9786 12.5945C23.1304 12.6574 23.2682 12.7495 23.3844 12.8656C23.5005 12.9818 23.5926 13.1196 23.6555 13.2714C23.7184 13.4231 23.7507 13.5858 23.7507 13.75C23.7507 13.9142 23.7184 14.0769 23.6555 14.2286C23.5926 14.3804 23.5005 14.5182 23.3844 14.6344L18.0172 20L23.3844 25.3656Z\" fill=\"#B5C0CD\"><\/path><\/svg><\/button><\/div>\n<\/div>\n<\/div>\n<p><script defer>\n    document.addEventListener('DOMContentLoaded', function() {\n        const videosCarouselSwiper = new Swiper('.video-carousel-swiper-block_69ef7150e2c17', {\n            slidesPerView: 1,\n            spaceBetween: 20,\n            loop: true,\n            pagination: {\n                el: '.swiper-article-video-carousel__pagination-container-block_69ef7150e2c17',\n                clickable: true,\n            },\n            navigation: {\n                nextEl: '.video-carousel-swiper-button-next-block_69ef7150e2c17',\n                prevEl: '.video-carousel-swiper-button-prev-block_69ef7150e2c17',\n            },\n            on: {\n                slideChangeTransitionStart: function () {\n                    const videos = this.el.querySelectorAll('video');\n                    videos.forEach(video => {\n                        if (!video.paused) {\n                            video.pause();\n                            video.currentTime = 0;\n                        }\n                    });\n                },\n            }\n        })\n    })\n<\/script><\/p>\n<h2 class=\"wp-block-heading\" id=\"pathogenese\">Pathogenese<\/h2>\n<ol class=\"wp-block-list\">\n<li><strong>\u041d\u0430\u0441\u043b\u0435\u0434\u0441\u0442\u0432\u0435\u043d\u043d\u044b\u0435 \u043c\u0443\u0442\u0430\u0446\u0438\u0438 (<em>SDHx<\/em>)<\/strong><\/li>\n<\/ol>\n<p>\u041c\u0443\u0442\u0430\u0446\u0438\u0438 <em>SDH<\/em> (\u043a\u043b\u044e\u0447\u0435\u0432\u043e\u0433\u043e \u0444\u0435\u0440\u043c\u0435\u043d\u0442\u0430 \u043a\u043e\u043c\u043f\u043b\u0435\u043a\u0441\u0430 II \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0439 \u0434\u044b\u0445\u0430\u0442\u0435\u043b\u044c\u043d\u043e\u0439 \u0446\u0435\u043f\u0438 \u0438 \u0446\u0438\u043a\u043b\u0430 \u041a\u0440\u0435\u0431\u0441\u0430) \u2192 \u043d\u0430\u043a\u043e\u043f\u043b\u0435\u043d\u0438\u0435 \u0441\u0443\u043a\u0446\u0438\u043d\u0430\u0442\u0430 (\u0434\u0435\u0439\u0441\u0442\u0432\u0443\u0435\u0442 \u043a\u0430\u043a <em>oncometabolite<\/em>) \u2192 \u0438\u043d\u0430\u043a\u0442\u0438\u0432\u0430\u0446\u0438\u044f \u043f\u0440\u043e\u043b\u0438\u043b\u0433\u0438\u0434\u0440\u043e\u043a\u0441\u0438\u043b\u0430\u0437 (PHDs) \u2014 \u0444\u0435\u0440\u043c\u0435\u043d\u0442\u043e\u0432, \u043a\u043e\u043d\u0442\u0440\u043e\u043b\u0438\u0440\u0443\u044e\u0449\u0438\u0445 \u0434\u0435\u0433\u0440\u0430\u0434\u0430\u0446\u0438\u044e HIF-1\u03b1 (\u0433\u0438\u043f\u043e\u043a\u0441\u0438\u044f-\u0438\u043d\u0434\u0443\u0446\u0438\u0440\u0443\u0435\u043c\u043e\u0433\u043e \u0444\u0430\u043a\u0442\u043e\u0440\u0430) \u2192 \u043d\u0430\u043a\u043e\u043f\u043b\u0435\u043d\u0438\u0435 HIF-1\u03b1 \u2192 \u043f\u0441\u0435\u0432\u0434\u043e\u0433\u0438\u043f\u043e\u043a\u0441\u0438\u044f \u2192 \u0430\u043a\u0442\u0438\u0432\u0430\u0446\u0438\u044f VEGF (\u0430\u043d\u0433\u0438\u043e\u0433\u0435\u043d\u0435\u0437) \/ GLUT1 (\u0433\u043b\u0438\u043a\u043e\u043b\u0438\u0437) \/ PDGF (\u043a\u043b\u0435\u0442\u043e\u0447\u043d\u0430\u044f \u043f\u0440\u043e\u043b\u0438\u0444\u0435\u0440\u0430\u0446\u0438\u044f) \u2192 \u043d\u0435\u043e\u043f\u043b\u0430\u0441\u0442\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u0442\u0440\u0430\u043d\u0441\u0444\u043e\u0440\u043c\u0430\u0446\u0438\u044f \u0445\u0435\u043c\u043e\u0440\u0435\u0446\u0435\u043f\u0442\u043e\u0440\u043d\u044b\u0445 \u043a\u043b\u0435\u0442\u043e\u043a \u0438 \u043e\u0431\u0440\u0430\u0437\u043e\u0432\u0430\u043d\u0438\u0435 \u043e\u043f\u0443\u0445\u043e\u043b\u0438.<\/p>\n<ol start=\"2\" class=\"wp-block-list\">\n<li><strong>Chronische Hypoxie<\/strong><\/li>\n<\/ol>\n<p>\u0413\u0438\u043f\u043e\u043a\u0441\u0438\u044f (\u0432\u044b\u0441\u043e\u0442\u0430, \u0425\u041e\u0411\u041b) \u2192 \u0441\u043d\u0438\u0436\u0435\u043d\u0438\u0435 pO\u2082 \u2192 \u0430\u043a\u0442\u0438\u0432\u0430\u0446\u0438\u044f \u043a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u044b\u0445 \u0440\u0435\u0446\u0435\u043f\u0442\u043e\u0440\u043e\u0432 \u2192 \u0433\u0438\u043f\u0435\u0440\u043f\u043b\u0430\u0437\u0438\u044f \u043a\u043b\u0435\u0442\u043e\u043a \u2192 \u043d\u0430\u043a\u043e\u043f\u043b\u0435\u043d\u0438\u0435 HIF-1\u03b1 \u2192 \u0430\u043d\u0433\u0438\u043e\u0433\u0435\u043d\u0435\u0437 \u0438 \u043d\u0435\u043e\u043f\u043b\u0430\u0437\u0438\u044f.\u00a0<\/p>\n<p>\u0412 \u0440\u0435\u0437\u0443\u043b\u044c\u0442\u0430\u0442\u0435 \u043e\u043f\u0443\u0445\u043e\u043b\u044c \u043f\u043e\u0441\u0442\u0435\u043f\u0435\u043d\u043d\u043e \u0443\u0432\u0435\u043b\u0438\u0447\u0438\u0432\u0430\u0435\u0442\u0441\u044f \u0432 \u0440\u0430\u0437\u043c\u0435\u0440\u0430\u0445. \u041f\u043e \u043c\u0435\u0440\u0435 \u0440\u043e\u0441\u0442\u0430 \u043e\u043d\u0430 \u043c\u043e\u0436\u0435\u0442 \u0434\u0435\u043c\u043e\u043d\u0441\u0442\u0440\u0438\u0440\u043e\u0432\u0430\u0442\u044c \u043b\u043e\u043a\u0430\u043b\u044c\u043d\u043e \u0438\u043d\u0432\u0430\u0437\u0438\u0432\u043d\u044b\u0439 \u0445\u0430\u0440\u0430\u043a\u0442\u0435\u0440, \u0432\u043f\u043b\u043e\u0442\u044c \u0434\u043e \u043e\u043a\u0440\u0443\u0436\u0435\u043d\u0438\u044f \u0438\u043b\u0438 \u0441\u0434\u0430\u0432\u043b\u0435\u043d\u0438\u044f \u0431\u043b\u0438\u0437\u043b\u0435\u0436\u0430\u0449\u0438\u0445 \u0430\u043d\u0430\u0442\u043e\u043c\u0438\u0447\u0435\u0441\u043a\u0438\u0445 \u0441\u0442\u0440\u0443\u043a\u0442\u0443\u0440, \u0442\u0430\u043a\u0438\u0445 \u043a\u0430\u043a \u0432\u043d\u0443\u0442\u0440\u0435\u043d\u043d\u044f\u044f \u0438 \u043d\u0430\u0440\u0443\u0436\u043d\u0430\u044f \u0441\u043e\u043d\u043d\u044b\u0435 \u0430\u0440\u0442\u0435\u0440\u0438\u0438, \u0431\u043b\u0443\u0436\u0434\u0430\u044e\u0449\u0438\u0439, \u043f\u043e\u0434\u044a\u044f\u0437\u044b\u0447\u043d\u044b\u0439 \u0438 \u044f\u0437\u044b\u043a\u043e\u0433\u043b\u043e\u0442\u043e\u0447\u043d\u044b\u0439 \u043d\u0435\u0440\u0432\u044b. \u042d\u0442\u043e \u043c\u043e\u0436\u0435\u0442 \u0432\u044b\u0437\u044b\u0432\u0430\u0442\u044c \u0441\u043e\u043e\u0442\u0432\u0435\u0442\u0441\u0442\u0432\u0443\u044e\u0449\u0443\u044e \u043d\u0435\u0432\u0440\u043e\u043b\u043e\u0433\u0438\u0447\u0435\u0441\u043a\u0443\u044e \u0438 \u0441\u043e\u0441\u0443\u0434\u0438\u0441\u0442\u0443\u044e \u0441\u0438\u043c\u043f\u0442\u043e\u043c\u0430\u0442\u0438\u043a\u0443.<\/p>\n<h2 class=\"wp-block-heading\" id=\"klassifikation-von-glomus-caroticum-paragangliomen\">Klassifikation von Glomus-caroticum-Paragangliomen<\/h2>\n<p>\u0423\u0438\u043b\u044c\u044f\u043c \u0428\u0430\u043c\u0431\u043b\u0438\u043d \u043f\u0440\u0435\u0434\u043b\u043e\u0436\u0438\u043b \u0434\u0435\u043b\u0438\u0442\u044c \u043f\u0430\u0440\u0430\u0433\u0430\u043d\u0433\u043b\u0438\u043e\u043c\u044b \u043a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u043e\u0433\u043e \u0442\u0435\u043b\u044c\u0446\u0430 \u043d\u0430 \u0442\u0440\u0438 \u0442\u0438\u043f\u0430 (Shamblin-\u043a\u043b\u0430\u0441\u0441\u0438\u0444\u0438\u043a\u0430\u0446\u0438\u044f):<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>\u0442\u0438\u043f I<\/strong>: \u043e\u0433\u0440\u0430\u043d\u0438\u0447\u0435\u043d\u043d\u044b\u0435 \u043e\u043f\u0443\u0445\u043e\u043b\u0438 \u0434\u043e 3,5 \u0441\u043c, \u0440\u044b\u0445\u043b\u043e \u0441\u0432\u044f\u0437\u0430\u043d\u043d\u044b\u0435 \u0441\u043e \u0441\u0442\u0435\u043d\u043a\u0430\u043c\u0438 \u0430\u0440\u0442\u0435\u0440\u0438\u0439;<\/li>\n<li><strong>\u0442\u0438\u043f II<\/strong>: 3,5\u20135 \u0441\u043c, \u0447\u0430\u0441\u0442\u0438\u0447\u043d\u043e \u043e\u0445\u0432\u0430\u0442\u044b\u0432\u0430\u044e\u0442 \u0441\u043e\u043d\u043d\u044b\u0435 \u0430\u0440\u0442\u0435\u0440\u0438\u0438, \u0438\u043c\u0435\u044e\u0442 \u0431\u043e\u043b\u0435\u0435 \u043f\u043b\u043e\u0442\u043d\u043e\u0435 \u0441\u0440\u0430\u0449\u0435\u043d\u0438\u0435 \u0441\u043e \u0441\u0442\u0435\u043d\u043a\u0430\u043c\u0438 \u0430\u0440\u0442\u0435\u0440\u0438\u0439;<\/li>\n<li><strong>\u0442\u0438\u043f III<\/strong>: \u0431\u043e\u043b\u0435\u0435 5 \u0441\u043c, \u043e\u0445\u0432\u0430\u0442\u044b\u0432\u0430\u044e\u0442 \u0441\u043e\u043d\u043d\u044b\u0435 \u0430\u0440\u0442\u0435\u0440\u0438\u0438 \u0438\/\u0438\u043b\u0438 \u0431\u043b\u0438\u0437\u043b\u0435\u0436\u0430\u0449\u0438\u0435 \u0441\u043e\u0441\u0443\u0434\u044b, \u043d\u0435\u0440\u0432\u044b \u0438\u043c\u0435\u044e \u0432\u044b\u0440\u0430\u0436\u0435\u043d\u043d\u043e \u043f\u043b\u043e\u0442\u043d\u043e\u0435 \u0441\u0440\u0430\u0449\u0435\u043d\u0438\u0435 \u0441 \u0434\u0430\u043d\u043d\u044b\u043c\u0438 \u0441\u0442\u0440\u0443\u043a\u0442\u0443\u0440\u0430\u043c\u0438.<\/li>\n<\/ul>\n<p>\u041a\u0440\u043e\u043c\u0435 \u0442\u043e\u0433\u043e, \u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0443 \u043c\u043e\u0436\u043d\u043e \u043a\u043b\u0430\u0441\u0441\u0438\u0444\u0438\u0446\u0438\u0440\u043e\u0432\u0430\u0442\u044c <strong>\u043f\u043e \u044d\u0442\u0438\u043e\u043b\u043e\u0433\u0438\u0438<\/strong>: \u0441\u043f\u043e\u0440\u0430\u0434\u0438\u0447\u0435\u0441\u043a\u0430\u044f (\u0434\u043e 85\u00a0%), \u0441\u0435\u043c\u0435\u0439\u043d\u0430\u044f (10\u201315\u00a0%), \u0433\u0438\u043f\u0435\u0440\u043f\u043b\u0430\u0441\u0442\u0438\u0447\u0435\u0441\u043a\u0430\u044f (1\u20135\u00a0%).<\/p>\n<div class=\"carousel-block\">\n<div class=\"swiper carousel-swiper carousel-swiper-block_69ef7150e7803\">\n<div class=\"swiper-wrapper\">\n<div class=\"swiper-slide image-carousel-slide\"><img decoding=\"async\" class=\"carousel-image\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/vascular-system\/paraganglioma\/chemodectoma-type-1.webp\" alt=\"\u0425\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 I \u0442\u0438\u043f\"><span class=\"small-text-article text-main-text-color\">\u0425\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 I \u0442\u0438\u043f<\/span><\/div>\n<div class=\"swiper-slide image-carousel-slide\"><img decoding=\"async\" class=\"carousel-image\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/vascular-system\/paraganglioma\/chemodectoma-type-3.webp\" alt=\"\u0425\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 III \u0442\u0438\u043f\"><span class=\"small-text-article text-main-text-color\">\u0425\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 III \u0442\u0438\u043f<\/span><\/div>\n<\/div>\n<\/div>\n<div class=\"swiper-article-carousel__controls\">\n<div class=\"swiper-article-carousel__pagination-container swiper-article-carousel__pagination-container-block_69ef7150e7803\"><\/div>\n<div class=\"swiper-article-carousel__arrows\"><button class=\"swiper__arrow swiper__arrow--prev carousel-swiper-button-prev swiper__arrow swiper__arrow--prev carousel-swiper-button-prev-block_69ef7150e7803\"><svg xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"40\" height=\"40\" viewbox=\"0 0 40 40\" fill=\"none\"><path d=\"M20 3.75C16.7861 3.75 13.6443 4.70305 10.972 6.48862C8.29969 8.27419 6.21689 10.8121 4.98696 13.7814C3.75704 16.7507 3.43524 20.018 4.06225 23.1702C4.68926 26.3224 6.23692 29.2179 8.50952 31.4905C10.7821 33.7631 13.6776 35.3107 16.8298 35.9378C19.982 36.5648 23.2493 36.243 26.2186 35.013C29.1879 33.7831 31.7258 31.7003 33.5114 29.028C35.297 26.3557 36.25 23.2139 36.25 20C36.2455 15.6916 34.5319 11.561 31.4855 8.51454C28.439 5.46806 24.3084 3.75455 20 3.75ZM23.3844 25.3656C23.5005 25.4818 23.5926 25.6196 23.6555 25.7714C23.7184 25.9231 23.7507 26.0858 23.7507 26.25C23.7507 26.4142 23.7184 26.5769 23.6555 26.7286C23.5926 26.8804 23.5005 27.0182 23.3844 27.1344C23.2682 27.2505 23.1304 27.3426 22.9786 27.4055C22.8269 27.4683 22.6643 27.5007 22.5 27.5007C22.3358 27.5007 22.1731 27.4683 22.0214 27.4055C21.8696 27.3426 21.7318 27.2505 21.6156 27.1344L15.3656 20.8844C15.2494 20.7683 15.1572 20.6304 15.0943 20.4787C15.0314 20.3269 14.999 20.1643 14.999 20C14.999 19.8357 15.0314 19.6731 15.0943 19.5213C15.1572 19.3696 15.2494 19.2317 15.3656 19.1156L21.6156 12.8656C21.7318 12.7495 21.8696 12.6574 22.0214 12.5945C22.1731 12.5317 22.3358 12.4993 22.5 12.4993C22.6643 12.4993 22.8269 12.5317 22.9786 12.5945C23.1304 12.6574 23.2682 12.7495 23.3844 12.8656C23.5005 12.9818 23.5926 13.1196 23.6555 13.2714C23.7184 13.4231 23.7507 13.5858 23.7507 13.75C23.7507 13.9142 23.7184 14.0769 23.6555 14.2286C23.5926 14.3804 23.5005 14.5182 23.3844 14.6344L18.0172 20L23.3844 25.3656Z\" fill=\"#B5C0CD\"><\/path><\/svg><\/button><button class=\"swiper__arrow swiper__arrow--next carousel-swiper-button-next swiper__arrow swiper__arrow--next carousel-swiper-button-next-block_69ef7150e7803\" tabindex=\"0\" aria-label=\"Next slide\"><svg xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"40\" height=\"40\" viewbox=\"0 0 40 40\" fill=\"none\"><path d=\"M20 3.75C16.7861 3.75 13.6443 4.70305 10.972 6.48862C8.29969 8.27419 6.21689 10.8121 4.98696 13.7814C3.75704 16.7507 3.43524 20.018 4.06225 23.1702C4.68926 26.3224 6.23692 29.2179 8.50952 31.4905C10.7821 33.7631 13.6776 35.3107 16.8298 35.9378C19.982 36.5648 23.2493 36.243 26.2186 35.013C29.1879 33.7831 31.7258 31.7003 33.5114 29.028C35.297 26.3557 36.25 23.2139 36.25 20C36.2455 15.6916 34.5319 11.561 31.4855 8.51454C28.439 5.46806 24.3084 3.75455 20 3.75ZM23.3844 25.3656C23.5005 25.4818 23.5926 25.6196 23.6555 25.7714C23.7184 25.9231 23.7507 26.0858 23.7507 26.25C23.7507 26.4142 23.7184 26.5769 23.6555 26.7286C23.5926 26.8804 23.5005 27.0182 23.3844 27.1344C23.2682 27.2505 23.1304 27.3426 22.9786 27.4055C22.8269 27.4683 22.6643 27.5007 22.5 27.5007C22.3358 27.5007 22.1731 27.4683 22.0214 27.4055C21.8696 27.3426 21.7318 27.2505 21.6156 27.1344L15.3656 20.8844C15.2494 20.7683 15.1572 20.6304 15.0943 20.4787C15.0314 20.3269 14.999 20.1643 14.999 20C14.999 19.8357 15.0314 19.6731 15.0943 19.5213C15.1572 19.3696 15.2494 19.2317 15.3656 19.1156L21.6156 12.8656C21.7318 12.7495 21.8696 12.6574 22.0214 12.5945C22.1731 12.5317 22.3358 12.4993 22.5 12.4993C22.6643 12.4993 22.8269 12.5317 22.9786 12.5945C23.1304 12.6574 23.2682 12.7495 23.3844 12.8656C23.5005 12.9818 23.5926 13.1196 23.6555 13.2714C23.7184 13.4231 23.7507 13.5858 23.7507 13.75C23.7507 13.9142 23.7184 14.0769 23.6555 14.2286C23.5926 14.3804 23.5005 14.5182 23.3844 14.6344L18.0172 20L23.3844 25.3656Z\" fill=\"#B5C0CD\"><\/path><\/svg><\/button><\/div>\n<\/div>\n<\/div>\n<p><script defer>\n    document.addEventListener('DOMContentLoaded', function() {\n        const imagesCarouselSwiper = new Swiper('.carousel-swiper-block_69ef7150e7803', {\n            slidesPerView: 1,\n            spaceBetween: 20,\n            loop: true,\n            pagination: {\n                el: '.swiper-article-carousel__pagination-container-block_69ef7150e7803',\n                clickable: true,\n            },\n            navigation: {\n                nextEl: '.carousel-swiper-button-next-block_69ef7150e7803',\n                prevEl: '.carousel-swiper-button-prev-block_69ef7150e7803',\n            },\n        })\n    })\n<\/script><\/p>\n<h2 class=\"wp-block-heading\" id=\"symptome\">Symptome<\/h2>\n<p>Das Glomus-caroticum-<span class=\"glossary-term\" data-title=\"Glomustumor\" data-tooltip=\"Als Glomustumor bzw. Paragangliom bezeichnet man einen seltenen, meist gutartigen Tumor, der von den Zellen der Paraganglien (Chemorezeptoren) ausgeht. Diese Zellen reagieren normalerweise auf Ver\u00e4nderungen der chemischen Zusammensetzung des Blutes und befinden sich entlang gro\u00dfer Gef\u00e4\u00dfe und Nerven.\" data-link=\"https:\/\/wiki.dev.voka.io\/de\/glossar\/glomustumor\/\">Paragangliom<\/span> kann \u00fcber einen langen Zeitraum asymptomatisch verlaufen. Mit zunehmendem Wachstum des Tumors k\u00f6nnen Beschwerden auftreten:  <\/p>\n<ul class=\"wp-block-list\">\n<li><strong>\u043f\u0430\u043b\u044c\u043f\u0438\u0440\u0443\u0435\u043c\u0430\u044f \u043e\u043f\u0443\u0445\u043e\u043b\u044c<\/strong> \u2014 \u043c\u0435\u0434\u043b\u0435\u043d\u043d\u043e \u0440\u0430\u0441\u0442\u0443\u0449\u0430\u044f, \u0431\u0435\u0437\u0431\u043e\u043b\u0435\u0437\u043d\u0435\u043d\u043d\u0430\u044f, \u043f\u0443\u043b\u044c\u0441\u0438\u0440\u0443\u044e\u0449\u0430\u044f \u043c\u0430\u0441\u0441\u0430 \u043d\u0430 \u0431\u043e\u043a\u043e\u0432\u043e\u0439 \u043f\u043e\u0432\u0435\u0440\u0445\u043d\u043e\u0441\u0442\u0438 \u0448\u0435\u0438 (\u0432 \u043e\u0431\u043b\u0430\u0441\u0442\u0438 \u0433\u0440\u0443\u0434\u0438\u043d\u043e-\u043a\u043b\u044e\u0447\u0438\u0447\u043d\u043e-\u0441\u043e\u0441\u0446\u0435\u0432\u0438\u0434\u043d\u043e\u0439 \u043c\u044b\u0448\u0446\u044b); \u200b<\/li>\n<li><strong>\u043d\u0435\u0432\u0440\u043e\u043b\u043e\u0433\u0438\u0447\u0435\u0441\u043a\u0438\u0435 \u0441\u0438\u043c\u043f\u0442\u043e\u043c\u044b <\/strong>\u2014 \u043e\u0441\u0438\u043f\u043b\u043e\u0441\u0442\u044c \u0433\u043e\u043b\u043e\u0441\u0430, \u0434\u0438\u0441\u0444\u0430\u0433\u0438\u044f, \u043e\u043d\u0435\u043c\u0435\u043d\u0438\u0435 \u044f\u0437\u044b\u043a\u0430, \u0432\u044b\u0437\u0432\u0430\u043d\u043d\u044b\u0435 \u043a\u043e\u043c\u043f\u0440\u0435\u0441\u0441\u0438\u0435\u0439 \u0447\u0435\u0440\u0435\u043f\u043d\u044b\u0445 \u043d\u0435\u0440\u0432\u043e\u0432 (IX\u2013XII); \u200b<\/li>\n<li><strong>\u0436<\/strong><strong>\u0430\u043b\u043e\u0431\u044b, \u0441\u0432\u044f\u0437\u0430\u043d\u043d\u044b\u0435 \u0441 \u0432\u044b\u0440\u0430\u0431\u043e\u0442\u043a\u043e\u0439 \u043a\u0430\u0442\u0435\u0445\u043e\u043b\u0430\u043c\u0438\u043d\u043e\u0432<\/strong> \u2014 \u0441\u0435\u0440\u0434\u0446\u0435\u0431\u0438\u0435\u043d\u0438\u0435, \u043f\u0440\u0438\u0441\u0442\u0443\u043f\u044b \u0430\u0440\u0442\u0435\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0439 \u0433\u0438\u043f\u0435\u0440\u0442\u0435\u043d\u0437\u0438\u0438, \u043f\u043e\u0442\u043b\u0438\u0432\u043e\u0441\u0442\u044c, \u0433\u043e\u043b\u043e\u0432\u043d\u0430\u044f \u0431\u043e\u043b\u044c, \u0442\u0440\u0435\u043c\u043e\u0440;<\/li>\n<li><strong>\u0440\u0435\u0434\u043a\u0438\u0435 \u043f\u0440\u043e\u044f\u0432\u043b\u0435\u043d\u0438\u044f<\/strong> \u2014 <strong>\u00a0<\/strong>\u0433\u043e\u043b\u043e\u0432\u043e\u043a\u0440\u0443\u0436\u0435\u043d\u0438\u0435, \u043e\u0431\u043c\u043e\u0440\u043e\u043a\u0438 \u043f\u0440\u0438 \u043a\u043e\u043c\u043f\u0440\u0435\u0441\u0441\u0438\u0438 \u043a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u043e\u0433\u043e \u0441\u0438\u043d\u0443\u0441\u0430.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"diagnostik-von-glomus-caroticum-paragangliomen\">Diagnostik von Glomus-caroticum-Paragangliomen<\/h2>\n<ul class=\"wp-block-list\">\n<li><strong>\u0424\u0438\u0437\u0438\u043a\u0430\u043b\u044c\u043d\u043e\u0435 \u043e\u0431\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u0435: <\/strong>\u043f\u043b\u043e\u0442\u043d\u0430\u044f, \u043f\u0443\u043b\u044c\u0441\u0438\u0440\u0443\u044e\u0449\u0430\u044f \u043e\u043f\u0443\u0445\u043e\u043b\u044c \u043d\u0430 \u0448\u0435\u0435, \u0441\u043c\u0435\u0449\u0430\u044e\u0449\u0430\u044f\u0441\u044f \u043f\u043e \u0433\u043e\u0440\u0438\u0437\u043e\u043d\u0442\u0430\u043b\u0438, \u043d\u043e \u043d\u0435 \u043f\u043e \u0432\u0435\u0440\u0442\u0438\u043a\u0430\u043b\u0438. \u200b<\/li>\n<li><strong>\u0423\u0417\u0418 \u0441 \u0434\u043e\u043f\u043f\u043b\u0435\u0440\u043e\u0433\u0440\u0430\u0444\u0438\u0435<\/strong>\u0439: \u0433\u0438\u043f\u0435\u0440\u0432\u0430\u0441\u043a\u0443\u043b\u044f\u0440\u043d\u0430\u044f \u043e\u043f\u0443\u0445\u043e\u043b\u044c \u0432 \u043e\u0431\u043b\u0430\u0441\u0442\u0438 \u0431\u0438\u0444\u0443\u0440\u043a\u0430\u0446\u0438\u0438 \u0441\u043e\u043d\u043d\u043e\u0439 \u0430\u0440\u0442\u0435\u0440\u0438\u0438. \u200b<\/li>\n<li><strong>\u041c\u0420\u0422 \u0441 \u043a\u043e\u043d\u0442\u0440\u0430\u0441\u0442\u043e\u043c<\/strong>: \u0445\u0430\u0440\u0430\u043a\u0442\u0435\u0440\u043d\u044b\u0439 \u00ab\u0441\u043e\u043b\u0435\u043d\u043e-\u043f\u0435\u0440\u0435\u0447\u043d\u044b\u0439\u00bb \u0432\u0438\u0434 \u043d\u0430 \u04221-\u0432\u0437\u0432\u0435\u0448\u0435\u043d\u043d\u044b\u0445 \u0438\u0437\u043e\u0431\u0440\u0430\u0436\u0435\u043d\u0438\u044f\u0445.<\/li>\n<li><strong>\u041a\u0422 \u0441 \u043a\u043e\u043d\u0442\u0440\u0430\u0441\u0442\u043e\u043c<\/strong>: \u043e\u043f\u0440\u0435\u0434\u0435\u043b\u0435\u043d\u0438\u0435 \u0441\u0442\u0435\u043f\u0435\u043d\u0438 \u0438\u043d\u0432\u0430\u0437\u0438\u0438 \u0432 \u0441\u043e\u0441\u0443\u0434\u044b, \u043e\u0446\u0435\u043d\u043a\u0430 Shamblin-\u043a\u043b\u0430\u0441\u0441\u0438\u0444\u0438\u043a\u0430\u0446\u0438\u0438. \u200b\u041f\u043e\u0441\u0442\u0440\u043e\u0435\u043d\u0438\u0435 3D-\u043c\u043e\u0434\u0435\u043b\u0438 \u0434\u043b\u044f \u043f\u043b\u0430\u043d\u0438\u0440\u043e\u0432\u0430\u043d\u0438\u044f \u043e\u043f\u0435\u0440\u0430\u0446\u0438\u0438.<\/li>\n<li><strong>\u0410\u043d\u0433\u0438\u043e\u0433\u0440\u0430\u0444\u0438\u044f<\/strong>: \u0432\u044b\u044f\u0432\u043b\u0435\u043d\u0438\u0435 \u00ab\u0437\u043d\u0430\u043a\u0430 \u043b\u0438\u0440\u044b\u00bb \u2014 \u0440\u0430\u0441\u0445\u043e\u0436\u0434\u0435\u043d\u0438\u044f \u0432\u043d\u0443\u0442\u0440\u0435\u043d\u043d\u0435\u0439 \u0438 \u043d\u0430\u0440\u0443\u0436\u043d\u043e\u0439 \u0441\u043e\u043d\u043d\u044b\u0445 \u0430\u0440\u0442\u0435\u0440\u0438\u0439. \u041f\u043e\u0437\u0432\u043e\u043b\u044f\u0435\u0442 \u043e\u0446\u0435\u043d\u0438\u0442\u044c \u043d\u0435\u043e\u0431\u0445\u043e\u0434\u0438\u043c\u043e\u0441\u0442\u044c\/\u0432\u043e\u0437\u043c\u043e\u0436\u043d\u043e\u0441\u0442\u044c \u044d\u043c\u0431\u043e\u043b\u0438\u0437\u0430\u0446\u0438\u0438 \u0434\u0430\u043d\u043d\u043e\u0439 \u0437\u043e\u043d\u044b \u043a\u0430\u043a \u044d\u0442\u0430\u043f\u0430 \u043f\u0435\u0440\u0435\u0434 \u043e\u043f\u0435\u0440\u0430\u0442\u0438\u0432\u043d\u044b\u043c \u0432\u043c\u0435\u0448\u0430\u0442\u0435\u043b\u044c\u0441\u0442\u0432\u043e\u043c. \u200b<\/li>\n<li><strong>\u041f\u042d\u0422-\u041a\u0422 \u0441 <\/strong><strong><sup>68<\/sup><\/strong><strong>Ga-DOTATATE<\/strong>: \u043f\u0440\u0438 \u043f\u043e\u0434\u043e\u0437\u0440\u0435\u043d\u0438\u0438 \u043d\u0430 \u043c\u043d\u043e\u0436\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u044b\u0435 \u0438\u043b\u0438 \u043c\u0435\u0442\u0430\u0441\u0442\u0430\u0442\u0438\u0447\u0435\u0441\u043a\u0438\u0435 \u043e\u0447\u0430\u0433\u0438.. \u200b<\/li>\n<li><strong>\u041b\u0430\u0431\u043e\u0440\u0430\u0442\u043e\u0440\u043d\u044b\u0435 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u044f<\/strong>: \u043e\u043f\u0440\u0435\u0434\u0435\u043b\u0435\u043d\u0438\u0435 \u0443\u0440\u043e\u0432\u043d\u044f \u043c\u0435\u0442\u0430\u043d\u0435\u0444\u0440\u0438\u043d\u043e\u0432 \u0438 \u043d\u043e\u0440\u043c\u0435\u0442\u0430\u043d\u0435\u0444\u0440\u0438\u043d\u043e\u0432 \u0432 \u043f\u043b\u0430\u0437\u043c\u0435 \u0438 \u043c\u043e\u0447\u0435 \u043f\u0440\u0438 \u043f\u043e\u0434\u043e\u0437\u0440\u0435\u043d\u0438\u0438 \u043d\u0430 \u0441\u0435\u043a\u0440\u0435\u0442\u0438\u0440\u0443\u044e\u0449\u0443\u044e \u043e\u043f\u0443\u0445\u043e\u043b\u044c.\u200b<\/li>\n<li><strong>\u0413\u0435\u043d\u0435\u0442\u0438\u0447\u0435\u0441\u043a\u043e\u0435 \u0442\u0435\u0441\u0442\u0438\u0440\u043e\u0432\u0430\u043d\u0438\u0435<\/strong> \u043d\u0430 \u043c\u0443\u0442\u0430\u0446\u0438\u0438 \u0432 \u0433\u0435\u043d\u0430\u0445 <em>SDH<\/em> \u043f\u0440\u0438 \u043d\u0430\u043b\u0438\u0447\u0438\u0438 \u0441\u0435\u043c\u0435\u0439\u043d\u043e\u0433\u043e \u0430\u043d\u0430\u043c\u043d\u0435\u0437\u0430 \u0438\u043b\u0438 \u043c\u043d\u043e\u0436\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u044b\u0445 \u043e\u043f\u0443\u0445\u043e\u043b\u0435\u0439.<\/li>\n<\/ul>\n<div class=\"social-banner-block\">\n<div class=\"social-banner-content\">\n<p class=\"h5-title text-black\">Weitere wissenschaftlich korrekte Inhalte finden Sie in unseren sozialen Medien<\/p>\n<p><span class=\"social-banner-text text-grey\">Abonnieren Sie und verpassen Sie nicht die neuesten Ressourcen<\/span><\/p>\n<div class=\"social-links-wrapper\"><a class=\"social-icon-link\" href=\"https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/facebook.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.instagram.com\/voka.io\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/insta.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.linkedin.com\/company\/voka-io\/posts\/?feedView=all\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/linkedin.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.youtube.com\/@vokaio\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/youtube.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.pinterest.com\/voka3danatomyandpathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/pinterest.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.tiktok.com\/@voka.io\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/tiktok.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/discord.gg\/7ejUpq8DRR\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/discord.svg\" alt=\"social link\"><\/a><\/div>\n<\/div>\n<p><img decoding=\"async\" class=\"social-banner-image\" loading=\"lazy\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/social-media-banner-mobile-image.webp\" alt=\"Banner background\"><\/div>\n<h2 class=\"wp-block-heading\" id=\"behandlung\">Behandlung<\/h2>\n<p>Die Behandlung eines Glomus-caroticum-Paraganglioms h\u00e4ngt von der Gr\u00f6\u00dfe des Tumors, dem klinischen Bild, dem Risiko f\u00fcr Komplikationen, der funktionellen Aktivit\u00e4t, dem genetischen Profil und dem Shamblin-Typ ab. Zu den wichtigsten Behandlungsmethoden geh\u00f6ren die chirurgische Entfernung, die pr\u00e4operative <span class=\"glossary-term\" data-title=\"Embolisation\" data-tooltip=\"Die Embolisation ist ein minimalinvasives endovaskul\u00e4res Verfahren, bei dem ein Blutgef\u00e4\u00df gezielt verschlossen wird, indem spezielle Materialien - Emboli - in das Gef\u00e4\u00dflumen eingebracht werden.\" data-link=\"https:\/\/wiki.dev.voka.io\/de\/glossar\/embolisation\/\">Embolisation<\/span> und in ausgew\u00e4hlten F\u00e4llen die Strahlen- oder Chemotherapie. <\/p>\n<ol class=\"wp-block-list\">\n<li><strong>Pr\u00e4operative Embolisation<\/strong><\/li>\n<\/ol>\n<p>\u041f\u0440\u0435\u0434\u043e\u043f\u0435\u0440\u0430\u0446\u0438\u043e\u043d\u043d\u0430\u044f \u044d\u043c\u0431\u043e\u043b\u0438\u0437\u0430\u0446\u0438\u044f \u043f\u0440\u043e\u0432\u043e\u0434\u0438\u0442\u0441\u044f \u0441 \u0446\u0435\u043b\u044c\u044e \u0441\u043d\u0438\u0436\u0435\u043d\u0438\u044f \u0432\u0430\u0441\u043a\u0443\u043b\u044f\u0440\u0438\u0437\u0430\u0446\u0438\u0438 \u043e\u043f\u0443\u0445\u043e\u043b\u0438, \u0443\u043c\u0435\u043d\u044c\u0448\u0435\u043d\u0438\u044f \u043e\u0431\u044a\u0435\u043c\u0430 \u0438\u043d\u0442\u0440\u0430\u043e\u043f\u0435\u0440\u0430\u0446\u0438\u043e\u043d\u043d\u043e\u0439 \u043a\u0440\u043e\u0432\u043e\u043f\u043e\u0442\u0435\u0440\u0438 \u0438 \u043e\u0431\u043b\u0435\u0433\u0447\u0435\u043d\u0438\u044f \u0432\u044b\u0434\u0435\u043b\u0435\u043d\u0438\u044f \u043e\u043f\u0443\u0445\u043e\u043b\u0438 \u043f\u0440\u0438 \u0445\u0438\u0440\u0443\u0440\u0433\u0438\u0438.<\/p>\n<p><strong>Indikationen<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>\u043e\u043f\u0443\u0445\u043e\u043b\u0438 Shamblin II\u2013III \u043a\u043b\u0430\u0441\u0441\u0430;<\/li>\n<li>\u0434\u0438\u0430\u043c\u0435\u0442\u0440 \u043e\u043f\u0443\u0445\u043e\u043b\u0438 > 3 \u0441\u043c;<\/li>\n<li>\u043d\u0430\u043b\u0438\u0447\u0438\u0435 \u0437\u043d\u0430\u0447\u0438\u043c\u043e\u0433\u043e \u0430\u0440\u0442\u0435\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0433\u043e \u043a\u0440\u043e\u0432\u043e\u0442\u043e\u043a\u0430 (\u043f\u043e \u0434\u0430\u043d\u043d\u044b\u043c \u041a\u0422\/\u0430\u043d\u0433\u0438\u043e\u0433\u0440\u0430\u0444\u0438\u0438);<\/li>\n<li>\u043f\u043b\u0430\u043d\u0438\u0440\u0443\u0435\u043c\u0430\u044f \u0440\u0435\u0437\u0435\u043a\u0446\u0438\u044f \u0441 \u0440\u0435\u043a\u043e\u043d\u0441\u0442\u0440\u0443\u043a\u0446\u0438\u0435\u0439 \u0441\u043e\u0441\u0443\u0434\u043e\u0432.<\/li>\n<\/ul>\n<p><strong>Kontraindikationen<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>\u043e\u043f\u0443\u0445\u043e\u043b\u0438 Shamblin I;<\/li>\n<li>\u043e\u0442\u0441\u0443\u0442\u0441\u0442\u0432\u0438\u0435 \u0430\u0440\u0442\u0435\u0440\u0438\u0430\u043b\u044c\u043d\u043e\u0433\u043e \u043a\u043e\u043c\u043f\u043e\u043d\u0435\u043d\u0442\u0430 (\u043d\u0438\u0437\u043a\u0430\u044f \u0432\u0430\u0441\u043a\u0443\u043b\u044f\u0440\u0438\u0437\u0430\u0446\u0438\u044f);<\/li>\n<li>\u0430\u043d\u0430\u0441\u0442\u043e\u043c\u043e\u0437\u044b \u0441 \u0446\u0435\u0440\u0435\u0431\u0440\u0430\u043b\u044c\u043d\u043e\u0439 \u0446\u0438\u0440\u043a\u0443\u043b\u044f\u0446\u0438\u0435\u0439 \u2014 \u0440\u0438\u0441\u043a \u044d\u043c\u0431\u043e\u043b\u0438\u0437\u0430\u0446\u0438\u0438 \u0433\u043e\u043b\u043e\u0432\u043d\u043e\u0433\u043e \u043c\u043e\u0437\u0433\u0430.<\/li>\n<\/ul>\n<p>\u0412\u044b\u043f\u043e\u043b\u043d\u044f\u0435\u0442\u0441\u044f \u0441\u0435\u043b\u0435\u043a\u0442\u0438\u0432\u043d\u0430\u044f \u0430\u043d\u0433\u0438\u043e\u0433\u0440\u0430\u0444\u0438\u044f \u043d\u0430\u0440\u0443\u0436\u043d\u043e\u0439 \u0441\u043e\u043d\u043d\u043e\u0439 \u0430\u0440\u0442\u0435\u0440\u0438\u0438. \u0427\u0435\u0440\u0435\u0437 \u043c\u0438\u043a\u0440\u043e\u043a\u0430\u0442\u0435\u0442\u0435\u0440 \u043e\u0441\u0443\u0449\u0435\u0441\u0442\u0432\u043b\u044f\u0435\u0442\u0441\u044f \u0432\u0432\u0435\u0434\u0435\u043d\u0438\u0435 \u044d\u043c\u0431\u043e\u043b\u0438\u0437\u0438\u0440\u0443\u044e\u0449\u0438\u0445 \u0430\u0433\u0435\u043d\u0442\u043e\u0432: \u043f\u043e\u043b\u0438\u0432\u0438\u043d\u0438\u043b\u0430\u043b\u043a\u043e\u0433\u043e\u043b\u044c\u043d\u044b\u0445 \u0447\u0430\u0441\u0442\u0438\u0446 (PVA), \u043c\u0438\u043a\u0440\u043e\u0441\u0444\u0435\u0440, \u0440\u0435\u0436\u0435 \u2014 \u043a\u043b\u0435\u044f \u0438\u043b\u0438 \u0441\u043f\u0438\u0440\u0430\u043b\u0435\u0439. \u041a\u043e\u043d\u0442\u0440\u043e\u043b\u044c\u043d\u0430\u044f \u0430\u043d\u0433\u0438\u043e\u0433\u0440\u0430\u0444\u0438\u044f \u043f\u043e\u0434\u0442\u0432\u0435\u0440\u0436\u0434\u0430\u0435\u0442 \u0440\u0435\u0434\u0443\u043a\u0446\u0438\u044e \u043a\u0440\u043e\u0432\u043e\u0442\u043e\u043a\u0430. \u041e\u043f\u0435\u0440\u0430\u0446\u0438\u044f \u043f\u0440\u043e\u0432\u043e\u0434\u0438\u0442\u0441\u044f \u0432 \u0442\u0435\u0447\u0435\u043d\u0438\u0435 24\u201348 \u0447\u0430\u0441\u043e\u0432 \u043f\u043e\u0441\u043b\u0435 \u044d\u043c\u0431\u043e\u043b\u0438\u0437\u0430\u0446\u0438\u0438, \u043f\u043e\u043a\u0430 \u0441\u043e\u0445\u0440\u0430\u043d\u044f\u0435\u0442\u0441\u044f \u044d\u0444\u0444\u0435\u043a\u0442.<\/p>\n<ol start=\"2\" class=\"wp-block-list\">\n<li><strong>Chirurgische Behandlung <\/strong><\/li>\n<\/ol>\n<p><strong>Indikationen<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>\u0441\u0438\u043c\u043f\u0442\u043e\u043c\u043d\u044b\u0435 \u043e\u043f\u0443\u0445\u043e\u043b\u0438 (\u0431\u043e\u043b\u044c, \u0434\u0438\u0441\u0444\u0430\u0433\u0438\u044f, \u043d\u0430\u0440\u0443\u0448\u0435\u043d\u0438\u0435 \u0440\u0435\u0447\u0438);<\/li>\n<li>\u0431\u044b\u0441\u0442\u0440\u044b\u0439 \u0440\u043e\u0441\u0442 \u043e\u043f\u0443\u0445\u043e\u043b\u0438;<\/li>\n<li>\u043e\u043f\u0443\u0445\u043e\u043b\u0438 > 2,5\u20133 \u0441\u043c (\u0434\u0430\u0436\u0435 \u0431\u0435\u0441\u0441\u0438\u043c\u043f\u0442\u043e\u043c\u043d\u044b\u0435);<\/li>\n<li>\u043f\u043e\u0434\u0442\u0432\u0435\u0440\u0436\u0434\u0435\u043d\u043d\u0430\u044f \u0430\u043a\u0442\u0438\u0432\u043d\u043e\u0441\u0442\u044c \u043f\u043e \u041f\u042d\u0422 \u0438\u043b\u0438 \u0431\u0438\u043e\u0445\u0438\u043c\u0438\u0438;<\/li>\n<li>\u043f\u043e\u0434\u0442\u0432\u0435\u0440\u0436\u0434\u0435\u043d\u043d\u0430\u044f \u043c\u0443\u0442\u0430\u0446\u0438\u044f SDHB (\u0440\u0438\u0441\u043a \u0437\u043b\u043e\u043a\u0430\u0447\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u043e\u0441\u0442\u0438);<\/li>\n<li>\u0432\u043e\u0437\u0440\u0430\u0441\u0442 < 60 \u043b\u0435\u0442.<\/li>\n<\/ul>\n<p><strong>Arten der chirurgischen Behandlung<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>\u042d\u043a\u0441\u0442\u0440\u0430\u043a\u0430\u043f\u0441\u0443\u043b\u044f\u0440\u043d\u0430\u044f \u0440\u0435\u0437\u0435\u043a\u0446\u0438\u044f \u043e\u043f\u0443\u0445\u043e\u043b\u0438<\/strong>. \u0421\u0442\u0430\u043d\u0434\u0430\u0440\u0442 \u0434\u043b\u044f Shamblin I\u2013II, \u0441\u043e\u0445\u0440\u0430\u043d\u0435\u043d\u0438\u0435 \u0441\u043e\u0441\u0443\u0434\u043e\u0432, \u043c\u0438\u043d\u0438\u043c\u0430\u043b\u044c\u043d\u044b\u0439 \u0440\u0438\u0441\u043a.<\/li>\n<li><strong>\u0420\u0435\u0437\u0435\u043a\u0446\u0438\u044f \u0441\u043e\u043d\u043d\u043e\u0439 \u0430\u0440\u0442\u0435\u0440\u0438\u0438 \u0441 \u0440\u0435\u043a\u043e\u043d\u0441\u0442\u0440\u0443\u043a\u0446\u0438\u0435\u0439<\/strong>. \u0427\u0430\u0449\u0435 \u043f\u0440\u0438 Shamblin III. \u041f\u043e\u0441\u043b\u0435 \u0440\u0435\u0437\u0435\u043a\u0446\u0438\u0438 \u0443\u0447\u0430\u0441\u0442\u043a\u0430 \u0441\u043e\u043d\u043d\u043e\u0439 \u0430\u0440\u0442\u0435\u0440\u0438\u0438 \u0432\u044b\u043f\u043e\u043b\u043d\u044f\u0435\u0442\u0441\u044f \u043f\u0440\u043e\u0442\u0435\u0437\u0438\u0440\u043e\u0432\u0430\u043d\u0438\u0435 (Dacron, PTFE).\u00a0<\/li>\n<li><strong>Neuromonitoring und Mikrochirurgie<\/strong>. Diese Verfahren werden bei unmittelbarer N\u00e4he zu Hirnnerven (IX-XII) eingesetzt.<\/li>\n<\/ul>\n<p><strong>M\u00f6gliche Komplikationen<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>\u043a\u0440\u043e\u0432\u043e\u0442\u0435\u0447\u0435\u043d\u0438\u0435 (\u043e\u0441\u043e\u0431\u0435\u043d\u043d\u043e \u043f\u0440\u0438 \u043d\u0435\u0434\u043e\u0441\u0442\u0430\u0442\u043e\u0447\u043d\u043e\u0439 \u044d\u043c\u0431\u043e\u043b\u0438\u0437\u0430\u0446\u0438\u0438);<\/li>\n<li>\u043f\u043e\u0432\u0440\u0435\u0436\u0434\u0435\u043d\u0438\u0435 \u0447\u0435\u0440\u0435\u043f\u043d\u044b\u0445 \u043d\u0435\u0440\u0432\u043e\u0432 (IX\u2013XII) \u2014 \u0434\u043e 30\u00a0% \u043f\u0440\u0438 \u043a\u0440\u0443\u043f\u043d\u044b\u0445 \u043e\u043f\u0443\u0445\u043e\u043b\u044f\u0445;<\/li>\n<li>\u0438\u043d\u0441\u0443\u043b\u044c\u0442 (\u043f\u0440\u0438 \u043d\u0430\u0440\u0443\u0448\u0435\u043d\u0438\u0438 \u043a\u043e\u043b\u043b\u0430\u0442\u0435\u0440\u0430\u043b\u044c\u043d\u043e\u0433\u043e \u043a\u0440\u043e\u0432\u043e\u0442\u043e\u043a\u0430);<\/li>\n<li>\u0440\u0435\u0446\u0438\u0434\u0438\u0432 (\u0440\u0435\u0434\u043a\u043e, \u043f\u0440\u0438 \u043d\u0435\u043f\u043e\u043b\u043d\u043e\u0439 \u0440\u0435\u0437\u0435\u043a\u0446\u0438\u0438).<\/li>\n<\/ul>\n<ol start=\"3\" class=\"wp-block-list\">\n<li><strong>Chemotherapie <\/strong><\/li>\n<\/ol>\n<p>Dieses Verfahren ist keine Standardbehandlung f\u00fcr ein Glomus-caroticum-Paragangliom, da die meisten Tumoren langsam wachsen und von Natur aus gutartig sind. In seltenen F\u00e4llen eines b\u00f6sartigen Verlaufs (schnelles Fortschreiten, metastasierende L\u00e4sionen) oder bei inoperablen metastasierenden Formen kann jedoch eine systemische Therapie eingesetzt werden. <\/p>\n<ol start=\"4\" class=\"wp-block-list\">\n<li><strong><strong>\u0420\u0430\u0434\u0438\u043e\u043d\u0443\u043a\u043b\u0438\u0434\u043d\u0430\u044f \u0442\u0435\u0440\u0430\u043f\u0438\u044f \u00b9\u2077\u2077Lu-DOTATATE (PRRT)\u00a0<\/strong><\/strong><\/li>\n<\/ol>\n<p>Diese Behandlungsmethode wird bei Vorliegen einer Somatostatinrezeptor-Expression eingesetzt, die durch PET mit \u2076\u2078Ga-DOTATATE nachgewiesen wurde.<\/p>\n<div>\n<h2 class=\"faq-title h2-article\" id=\"faq\">FAQ<\/h2>\n<div class=\"faq-section\">\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">1. Ist ein Glomus-caroticum-Paragangliom ein b\u00f6sartiger Tumor?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">\u0412 \u0431\u043e\u043b\u044c\u0448\u0438\u043d\u0441\u0442\u0432\u0435 \u0441\u043b\u0443\u0447\u0430\u0435\u0432 \u2014 \u043d\u0435\u0442. \u041a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u0430\u044f \u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430 \u043e\u0442\u043d\u043e\u0441\u0438\u0442\u0441\u044f \u043a \u0434\u043e\u0431\u0440\u043e\u043a\u0430\u0447\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u044b\u043c, \u043c\u0435\u0434\u043b\u0435\u043d\u043d\u043e \u0440\u0430\u0441\u0442\u0443\u0449\u0438\u043c \u043e\u043f\u0443\u0445\u043e\u043b\u044f\u043c. \u041e\u0434\u043d\u0430\u043a\u043e \u043f\u0440\u0438 \u043d\u0430\u043b\u0438\u0447\u0438\u0438 \u043c\u0443\u0442\u0430\u0446\u0438\u0439 \u0433\u0435\u043d\u0430 <em>SDHB<\/em> \u0432\u043e\u0437\u043c\u043e\u0436\u0435\u043d \u0437\u043b\u043e\u043a\u0430\u0447\u0435\u0441\u0442\u0432\u0435\u043d\u043d\u044b\u0439 \u043f\u043e\u0442\u0435\u043d\u0446\u0438\u0430\u043b \u0441 \u043c\u0435\u0442\u0430\u0441\u0442\u0430\u0437\u0438\u0440\u043e\u0432\u0430\u043d\u0438\u0435\u043c.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">2. \u041c\u043e\u0436\u043d\u043e \u043b\u0438 \u043f\u0440\u043e\u0441\u0442\u043e \u043d\u0430\u0431\u043b\u044e\u0434\u0430\u0442\u044c \u043a\u0430\u0440\u043e\u0442\u0438\u0434\u043d\u0443\u044e \u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0443, \u043d\u0435 \u0443\u0434\u0430\u043b\u044f\u044f \u0435\u0435?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">\u0414\u0430, \u0432 \u043d\u0435\u043a\u043e\u0442\u043e\u0440\u044b\u0445 \u0441\u043b\u0443\u0447\u0430\u044f\u0445 \u0432\u043e\u0437\u043c\u043e\u0436\u043d\u043e \u0430\u043a\u0442\u0438\u0432\u043d\u043e\u0435 \u043d\u0430\u0431\u043b\u044e\u0434\u0435\u043d\u0438\u0435, \u043e\u0441\u043e\u0431\u0435\u043d\u043d\u043e \u0435\u0441\u043b\u0438 \u043e\u043f\u0443\u0445\u043e\u043b\u044c \u043d\u0435\u0431\u043e\u043b\u044c\u0448\u0430\u044f (< 2,5 \u0441\u043c), \u0431\u0435\u0441\u0441\u0438\u043c\u043f\u0442\u043e\u043c\u043d\u0430\u044f, \u0443 \u043f\u0430\u0446\u0438\u0435\u043d\u0442\u0430 \u043f\u043e\u0436\u0438\u043b\u043e\u0439 \u0432\u043e\u0437\u0440\u0430\u0441\u0442 \u0438\u043b\u0438 \u0435\u0441\u0442\u044c \u043f\u0440\u043e\u0442\u0438\u0432\u043e\u043f\u043e\u043a\u0430\u0437\u0430\u043d\u0438\u044f \u043a \u043e\u043f\u0435\u0440\u0430\u0446\u0438\u0438. \u041e\u0434\u043d\u0430\u043a\u043e \u043f\u0440\u0438 \u043f\u0440\u0438\u0437\u043d\u0430\u043a\u0430\u0445 \u0440\u043e\u0441\u0442\u0430 \u0438\u043b\u0438 \u043a\u043e\u043c\u043f\u0440\u0435\u0441\u0441\u0438\u0438 \u0441\u0442\u0440\u0443\u043a\u0442\u0443\u0440 \u0448\u0435\u0438 \u0442\u0440\u0435\u0431\u0443\u0435\u0442\u0441\u044f \u043b\u0435\u0447\u0435\u043d\u0438\u0435.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">3. Ist ein chirurgischer Eingriff zur Entfernung eines Glomus-caroticum-Paraganglioms gef\u00e4hrlich?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Die Risiken h\u00e4ngen von der Gr\u00f6\u00dfe und Lage des Tumors ab. Bei gro\u00dfen Raumforderungen sind Komplikationen wie Verletzung von Hirnnerven, Blutungen und isch\u00e4mische Ereignisse m\u00f6glich. Um die Risiken zu verringern, wird h\u00e4ufig eine pr\u00e4operative Embolisation durchgef\u00fchrt.  <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">4. Ist es notwendig, dass andere Familienmitglieder untersucht werden, wenn bei mir ein Glomus-caroticum-Paragangliom diagnostiziert wurde?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">\u0415\u0441\u043b\u0438 \u0443 \u0432\u0430\u0441 \u0432\u044b\u044f\u0432\u043b\u0435\u043d\u0430 \u043d\u0430\u0441\u043b\u0435\u0434\u0441\u0442\u0432\u0435\u043d\u043d\u0430\u044f \u043c\u0443\u0442\u0430\u0446\u0438\u044f (\u043d\u0430\u043f\u0440\u0438\u043c\u0435\u0440, <em>SDHD<\/em>, <em>SDHB<\/em>), \u0440\u0435\u043a\u043e\u043c\u0435\u043d\u0434\u0443\u0435\u0442\u0441\u044f \u0433\u0435\u043d\u0435\u0442\u0438\u0447\u0435\u0441\u043a\u043e\u0435 \u043a\u043e\u043d\u0441\u0443\u043b\u044c\u0442\u0438\u0440\u043e\u0432\u0430\u043d\u0438\u0435 \u0438 \u043e\u0431\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u0435 \u0431\u043b\u0438\u0436\u0430\u0439\u0448\u0438\u0445 \u0440\u043e\u0434\u0441\u0442\u0432\u0435\u043d\u043d\u0438\u043a\u043e\u0432, \u043f\u043e\u0441\u043a\u043e\u043b\u044c\u043a\u0443 \u0437\u0430\u0431\u043e\u043b\u0435\u0432\u0430\u043d\u0438\u0435 \u043c\u043e\u0436\u0435\u0442 \u0431\u044b\u0442\u044c \u0441\u0435\u043c\u0435\u0439\u043d\u044b\u043c.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">5. Wie unterscheidet man ein Glomus-caroticum-Paragangliom von anderen Halstumoren?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Ein Glomus-caroticum-Tumor befindet sich in der Regel an der Bifurkation der A. carotis communis, ist pulsierend, l\u00e4sst sich horizontal, aber nicht vertikal verschieben und zeigt bei <span class=\"glossary-term\" data-title=\"Computertomographie\" data-tooltip=\"Die Computertomographie ist ein bildgebendes Verfahren, bei dem mittels R\u00f6ntgenstrahlung in Schichten Bilder (Schnitte) von inneren Organen und Geweben erstellt werden. Dies ist eines der wichtigsten bildgebenden Verfahren in der modernen Medizin, das eine hohe Aussagekraft aufweist.\" data-link=\"https:\/\/wiki.dev.voka.io\/de\/glossar\/ct-computertomographie\/\">CT<\/span>\/<span class=\"glossary-term\" data-title=\"MRT (Magnetresonanztomographie)\" data-tooltip=\"Die Magnetresonanztomographie (MRT oder MR) ist ein modernes, nicht-invasives Schnittbildverfahren, das zur hochdetaillierten Darstellung von inneren Organen und Geweben zum Einsatz kommt. Es basiert physikalisch auf den Prinzipien der Kernspinresonanz. Der entscheidende Vorteil der MRT ist, dass bei ihr keine ionisierende Strahlung (Radiation) genutzt wird.\" data-link=\"https:\/\/wiki.dev.voka.io\/de\/glossar\/mrt\/\">MRT<\/span> das charakteristische \u201eLyra-Zeichen\u201c. Die Diagnose wird durch bildgebende Verfahren und Angiographie gekl\u00e4rt. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">6. Kann ein Glomus-caroticum-Paragangliom Schmerzen oder Unwohlsein verursachen?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">In den meisten F\u00e4llen nicht, vor allem nicht im Fr\u00fchstadium. Allerdings kann der Tumor mit zunehmendem Wachstum Druck auf Nerven und Blutgef\u00e4\u00dfe aus\u00fcben, was zu Schmerzen, Heiserkeit, Schluckbeschwerden oder Schwindelgef\u00fchl f\u00fchren kann. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">7. Besteht das Risiko eines R\u00fcckfalls nach der Tumorentfernung?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">\u041f\u0440\u0438 \u043f\u043e\u043b\u043d\u043e\u043c \u0443\u0434\u0430\u043b\u0435\u043d\u0438\u0438 \u043e\u043f\u0443\u0445\u043e\u043b\u0438 \u0440\u0438\u0441\u043a \u0440\u0435\u0446\u0438\u0434\u0438\u0432\u0430 \u043d\u0438\u0437\u043a\u0438\u0439 (\u043c\u0435\u043d\u0435\u0435 5 %). \u041e\u0434\u043d\u0430\u043a\u043e \u043f\u0440\u0438 \u043d\u0435\u043f\u043e\u043b\u043d\u043e\u0439 \u0440\u0435\u0437\u0435\u043a\u0446\u0438\u0438, \u043d\u0430\u0441\u043b\u0435\u0434\u0441\u0442\u0432\u0435\u043d\u043d\u043e\u0439 \u0444\u043e\u0440\u043c\u0435 \u0438\u043b\u0438 \u043d\u0430\u043b\u0438\u0447\u0438\u0438 <em>SDHB<\/em>-\u043c\u0443\u0442\u0430\u0446\u0438\u0438, \u0432\u043e\u0437\u043c\u043e\u0436\u0435\u043d \u0440\u0435\u0446\u0438\u0434\u0438\u0432 \u0438\u043b\u0438 \u0440\u0430\u0437\u0432\u0438\u0442\u0438\u0435 \u043d\u043e\u0432\u044b\u0445 \u043e\u0447\u0430\u0433\u043e\u0432. \u0412 \u0442\u0430\u043a\u0438\u0445 \u0441\u043b\u0443\u0447\u0430\u044f\u0445 \u0432\u0430\u0436\u043d\u043e \u0434\u043e\u043b\u0433\u043e\u0441\u0440\u043e\u0447\u043d\u043e\u0435 \u043d\u0430\u0431\u043b\u044e\u0434\u0435\u043d\u0438\u0435.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"sources-list-block sources-list-hidden\" id=\"liste-der-quellen\">\n<div class=\"sources-list-content\">\n<div class=\"sources-list-title\">\n<p class=\"small-text-bold text-black sources-list-title-text\">Liste der Quellen<\/p>\n<div class=\"sources-expand-button-wrapper-mobile\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n<div class=\"sources-list-items\">\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">1.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>VOKA 3D Anatomy & Pathology \u2013 Complete Anatomy and Pathology 3D Atlas [Internet]. VOKA 3D Anatomy & Pathology. <\/cite><\/p>\n<p><span class=\"small-text-medium text-grey\">Available from: https:\/\/catalog.voka.io\/<\/span><\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">2.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Luna-Ortiz K, Reynoso-Nover\u00f3n N, Herrera-Ponzanelli C, Favila-Lira S, Luna-Peteuil Z, Herrera-Gomez A, et al. Sex differences according to ethnic presentation in carotid body tumors: a systematic literature review. Int J Otorhinolaryngol Head Neck Surg. 2022 Jun;8(6):527-531. doi: 10.18203\/issn.2454-5929.ijohns20221393. <\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">3.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Butt N, Baek WK, Lachkar S, Iwanaga J, Mian A, Blaak C, et al. The carotid body and associated tumors: updated review with clinical\/surgical significance. Br J Neurosurg. 2019 Oct;33(5):500-503. doi: 10.1080\/02688697.2019.1617404.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">4.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Darouassi Y, Alaoui M, Mliha Touati M, Al Maghraoui O, En-Nouali A, Bouaity B, Ammar H. Carotid Body Tumors: A Case Series and Review of the Literature. Ann Vasc Surg. 2017 Aug;43:265-271. doi: 10.1016\/j.avsg.2017.03.167.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">5.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Gonzalez-Urquijo M, Castro-Varela A, Barrios-Ruiz A, Hinojosa-Gonzalez DE, Salas AKG, Morales EA, et al. Current trends in carotid body tumors: comprehensive review. Head Neck. 2022 Oct;44(10):2316-2332. doi: 10.1002\/hed.27147.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">6.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Ozawa H. Current management of carotid body tumors. Auris Nasus Larynx. 2024 Jun;51(3):501-506. doi: 10.1016\/j.anl.2024.01.007.<\/cite><\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">7.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\"><cite>Piazza C, Lancini D, Tomasoni M, Zafereo M, Poorten VV, Hanna E, et al. Malignant carotid body tumors: what we know, what we do, and what we need to achieve. A systematic review of the literature. 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Epidemiologie \u00c4tiologie \u0413\u0435\u043d\u0435\u0442\u0438\u0447\u0435\u0441\u043a\u0438\u0435 \u043c\u0443\u0442\u0430\u0446\u0438\u0438 \u2014 \u0432\u0435\u0434\u0443\u0449\u0443\u044e \u0440\u043e\u043b\u044c \u0438\u0433\u0440\u0430\u044e\u0442 \u043c\u0443\u0442\u0430\u0446\u0438\u0438 \u0432 \u0433\u0435\u043d\u0430\u0445, \u043a\u043e\u0434\u0438\u0440\u0443\u044e\u0449\u0438\u0445 \u0441\u0443\u0431\u044a\u0435\u0434\u0438\u043d\u0438\u0446\u044b \u0441\u0443\u043a\u0446\u0438\u043d\u0430\u0442\u0434\u0435\u0433\u0438\u0434\u0440\u043e\u0433\u0435\u043d\u0430\u0437\u043d\u043e\u0433\u043e \u043a\u043e\u043c\u043f\u043b\u0435\u043a\u0441\u0430 (SDH), \u043a\u043e\u0442\u043e\u0440\u044b\u0439 \u0443\u0447\u0430\u0441\u0442\u0432\u0443\u0435\u0442 \u0432 \u0434\u044b\u0445\u0430\u0442\u0435\u043b\u044c\u043d\u043e\u0439 \u0446\u0435\u043f\u0438 \u043c\u0438\u0442\u043e\u0445\u043e\u043d\u0434\u0440\u0438\u0439 \u0438 \u043a\u043b\u0435\u0442\u043e\u0447\u043d\u043e\u043c \u043c\u0435\u0442\u0430\u0431\u043e\u043b\u0438\u0437\u043c\u0435. \u041e\u0441\u043d\u043e\u0432\u043d\u044b\u0435 \u0433\u0435\u043d\u044b: \u0421\u0438\u043d\u0434\u0440\u043e\u043c\u044b, \u0430\u0441\u0441\u043e\u0446\u0438\u0438\u0440\u043e\u0432\u0430\u043d\u043d\u044b\u0435 \u0441 \u0445\u0435\u043c\u043e\u0434\u0435\u043a\u0442\u043e\u043c\u0430\u043c\u0438:\u00a0 \u0425\u0440\u043e\u043d\u0438\u0447\u0435\u0441\u043a\u0430\u044f \u0433\u0438\u043f\u043e\u043a\u0441\u0438\u044f [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"template":"","diseases_category":[216],"class_list":["post-554","diseases_post","type-diseases_post","status-publish","hentry","diseases_category-gefaesssystem"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v25.0 (Yoast SEO v26.5) - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Paragangliom der Halsschlagader (Chemodektom) am Hals: Symptome, Diagnose, Behandlung<\/title>\n<meta name=\"description\" content=\"Das Paragangliom (Chemodectom) ist ein seltener, \u00fcberwiegend gutartiger Tumor der Chemorezeptorzellen im Bereich der Karotisgabel. 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