![\"\u062a\u0636\u062e\u0645](\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/acquired-heart-diseases\/hypertrophic-cardiomyopathy\/thickened-wall-of-left-ventricle-in-hcm-2.webp\")
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\n \u0627\u0644\u062c\u064a\u0646<\/strong><\/th>\n \u0627\u0644\u0628\u0631\u0648\u062a\u064a\u0646<\/strong><\/th>\n \u0645\u0639\u062f\u0644 \u0634\u064a\u0648\u0639 \u0627\u0644\u0637\u0641\u0631\u0627\u062a<\/strong><\/strong><\/th>\n<\/tr>\n<\/thead>\n\n \n MYH7<\/td>\n \u0633\u0644\u0633\u0644\u0629 \u0627\u0644\u0645\u064a\u0648\u0633\u064a\u0646 \u0627\u0644\u062b\u0642\u064a\u0644\u0629 \u0628\u064a\u062a\u0627 (\u03b2-MHC)<\/td>\n \u064a\u0645\u062b\u0644 \u0627\u0644\u062c\u064a\u0646\u0627\u0646 MYH7 \u0648MYBPC3 \u0646\u062d\u0648 70% \u0645\u0646 \u062d\u0627\u0644\u0627\u062a \u0627\u0644\u0637\u0641\u0631\u0627\u062a<\/td>\n<\/tr>\n \n MYBPC3<\/td>\n \u0628\u0631\u0648\u062a\u064a\u0646 \u0631\u0628\u0637 \u0627\u0644\u0645\u064a\u0648\u0633\u064a\u0646 \u0627\u0644\u0642\u0644\u0628\u064a<\/td>\n \u064a\u0645\u062b\u0644 \u0627\u0644\u062c\u064a\u0646\u0627\u0646 MYH7 \u0648MYBPC3 \u0646\u062d\u0648 70% \u0645\u0646 \u062d\u0627\u0644\u0627\u062a \u0627\u0644\u0637\u0641\u0631\u0627\u062a<\/td>\n<\/tr>\n \n TNNT2<\/td>\n \u062a\u0631\u0648\u0628\u0648\u0646\u064a\u0646 T \u0627\u0644\u0642\u0644\u0628\u064a<\/td>\n \u062d\u0648\u0627\u0644\u064a 5%<\/td>\n<\/tr>\n \n TNNI3<\/td>\n \u062a\u0631\u0648\u0628\u0648\u0646\u064a\u0646 I \u0627\u0644\u0642\u0644\u0628\u064a<\/td>\n <5%<\/td>\n<\/tr>\n \n TPM1<\/td>\n \u0627\u0644\u062a\u0631\u0648\u0628\u0648\u0645\u064a\u0648\u0632\u064a\u0646 (\u0628\u0631\u0648\u062a\u064a\u0646 \u0639\u0636\u0644\u064a)<\/td>\n <5%<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<\/figure>\n \n
\n\n
\n \u0627\u0644\u0645\u0631\u0636<\/strong><\/th>\n \u0622\u0644\u064a\u0629 \u0627\u0644\u0645\u0631\u0636<\/strong><\/th>\n \u0627\u0644\u062e\u0635\u0627\u0626\u0635 \u0627\u0644\u0645\u0645\u064a\u0632\u0629<\/strong><\/th>\n<\/tr>\n<\/thead>\n\n \n \u0645\u0631\u0636 \u0641\u0627\u0628\u0631\u064a<\/td>\n \u0645\u0631\u0636 \u062a\u062e\u0632\u064a\u0646 \u0644\u064a\u0632\u0648\u0632\u0648\u0645\u064a \u0648\u0631\u0627\u062b\u064a (\u0646\u0627\u062a\u062c \u0639\u0646 \u0646\u0642\u0635 \u0625\u0646\u0632\u064a\u0645 \u0623\u0644\u0641\u0627\u2013\u063a\u0627\u0644\u0627\u0643\u062a\u0648\u0632\u064a\u062f\u0627\u0632 A).<\/td>\n \u0639\u0644\u0627\u0645\u0627\u062a \u0627\u0644\u0625\u0635\u0627\u0628\u0629 \u0627\u0644\u062c\u0647\u0627\u0632\u064a\u0629 (\u0627\u0644\u0648\u0631\u0645 \u0627\u0644\u0648\u0639\u0627\u0626\u064a \u0627\u0644\u062b\u0624\u0644\u0648\u0644\u064a \u00ab\u0623\u0646\u062c\u064a\u0648\u0643\u064a\u0631\u0627\u062a\u0648\u0645\u0627\u00bb\u060c \u0627\u0644\u0627\u0639\u062a\u0644\u0627\u0644 \u0627\u0644\u0639\u0635\u0628\u064a\u060c \u0648\u0627\u0644\u0628\u064a\u0644\u0629 \u0627\u0644\u0628\u0631\u0648\u062a\u064a\u0646\u064a\u0629)<\/td>\n<\/tr>\n \n \u0627\u0644\u062f\u0627\u0621 \u0627\u0644\u0646\u0634\u0648\u0627\u0646\u064a \u0627\u0644\u0642\u0644\u0628\u064a<\/td>\n \u062a\u0631\u0633\u0628 \u0627\u0644\u0628\u0631\u0648\u062a\u064a\u0646 \u0627\u0644\u0646\u0634\u0648\u0627\u0646\u064a (AL\u060c \u200fATTR) \u0641\u064a \u0639\u0636\u0644\u0629 \u0627\u0644\u0642\u0644\u0628<\/td>\n \u062a\u0636\u062e\u0645 \u0627\u0644\u062c\u062f\u0631\u0627\u0646\u060c \u0648\u0627\u0646\u062e\u0641\u0627\u0636 \u0627\u0644\u0642\u062f\u0631\u0629 \u0627\u0644\u0627\u0646\u0642\u0628\u0627\u0636\u064a\u0629\u060c \u0648\u0627\u0644\u062e\u0644\u0644 \u0627\u0644\u0627\u0646\u0628\u0633\u0627\u0637\u064a<\/td>\n<\/tr>\n \n \u0631\u0646\u062d \u0641\u0631\u064a\u062f\u0631\u064a\u062e<\/td>\n \u0645\u0631\u0636 \u0635\u0628\u063a\u064a \u062c\u0633\u062f\u064a \u0645\u062a\u0646\u062d\u060c \u0646\u0627\u062c\u0645 \u0639\u0646 \u0637\u0641\u0631\u0627\u062a \u0641\u064a \u062c\u064a\u0646 \u200eFXN\u200e (\u0645\u0631\u0636 \u0645\u062a\u0642\u062f\u0631\u064a)<\/td>\n \u0627\u0644\u062a\u0646\u0643\u0633 \u0627\u0644\u0639\u0635\u0628\u064a \u0627\u0644\u0645\u062a\u0642\u062f\u0645 (\u0627\u0644\u0631\u0646\u062d\u060c \u0627\u0644\u0636\u0639\u0641 \u0648\u0627\u0644\u0636\u0645\u0648\u0631 \u0627\u0644\u0639\u0636\u0644\u064a\u060c \u0627\u0636\u0637\u0631\u0627\u0628 \u0627\u0644\u0643\u0644\u0627\u0645\u060c \u0648\u063a\u064a\u0631\u0647\u0627)<\/td>\n<\/tr>\n \n \u0623\u0645\u0631\u0627\u0636 \u062a\u062e\u0632\u064a\u0646 \u0627\u0644\u063a\u0644\u064a\u0643\u0648\u062c\u064a\u0646 (\u0645\u062b\u0644\u064b\u0627 \u062f\u0627\u0621 \u0628\u0648\u0645\u0628\u064a\u0647)<\/td>\n \u062a\u0631\u0627\u0643\u0645 \u0627\u0644\u063a\u0644\u064a\u0643\u0648\u062c\u064a\u0646 \u062f\u0627\u062e\u0644 \u0627\u0644\u062c\u0633\u064a\u0645\u0627\u062a \u0627\u0644\u062d\u0627\u0644\u0629 \u0641\u064a \u0627\u0644\u062e\u0644\u0627\u064a\u0627\u060c \u0648\u0644\u0627 \u0633\u064a\u0645\u0627 \u0641\u064a \u0627\u0644\u0639\u0636\u0644\u0627\u062a \u0648\u0627\u0644\u0642\u0644\u0628<\/td>\n \u063a\u0627\u0644\u0628\u064b\u0627 \u0645\u0627 \u064a\u0643\u0648\u0646 \u0645\u0635\u0627\u062d\u0628\u064b\u0627 \u0628\u0625\u0635\u0627\u0628\u0629 \u0627\u0644\u0639\u0636\u0644\u0627\u062a \u0627\u0644\u0647\u064a\u0643\u0644\u064a\u0629<\/td>\n<\/tr>\n \n \u0641\u0631\u0637 \u0636\u063a\u0637 \u0627\u0644\u062f\u0645 \u0627\u0644\u0634\u0631\u064a\u0627\u0646\u064a \u0627\u0644\u062c\u0647\u0627\u0632\u064a<\/td>\n \u0627\u0644\u062a\u0636\u062e\u0645 \u0627\u0644\u062a\u0641\u0627\u0639\u0644\u064a \u0644\u0639\u0636\u0644\u0629 \u0627\u0644\u0642\u0644\u0628<\/td>\n \u064a\u0643\u0648\u0646 \u063a\u0627\u0644\u0628\u064b\u0627 \u0645\u062a\u0645\u0627\u062b\u0644\u064b\u0627 \u0648\u0645\u0631\u062a\u0628\u0637\u064b\u0627 \u0628\u0633\u0648\u0627\u0628\u0642 \u0645\u0646 \u0641\u0631\u0637 \u0636\u063a\u0637 \u0627\u0644\u062f\u0645<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<\/figure>\n \n
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\u0627\u0644\u0622\u0644\u064a\u0629 \u0627\u0644\u0625\u0645\u0631\u0627\u0636\u064a\u0629<\/h2>\n
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![\"\u0627\u0646\u0633\u062f\u0627\u062f](\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/en\/acquired-heart-diseases\/hypertrophic-cardiomyopathy\/obstruction-of-outflow-tract-due-to-thickening-of-interventricular-septum.webp\")
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